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(1970). The estimation of postmenstrual age: a comprehensive review. Developmental Medicine and Child Neurology, 12, 697-729.","journal-title":"Developmental Medicine and Child Neurology"},{"issue":"45","key":"ref_2","first-page":"91","volume":"44","author":"Davies, P.A.; Robinson, R.J.; Scopes, J.W.; Tizard, J.P.M.; Wigglesworth, J.S.","year":"1972","unstructured":"Davies, P. A., Robinson, R. J., Scopes, J. W., Tizard, J. P. M., and Wigglesworth, J. S. (1972). The Medical Care of Newborn Babies, pp. 91-92. Clinics in Developmental Medicine No. 44\/45. Heinemann, London.","journal-title":"The Medical Care of Newborn Babies; Clinics in Developmental Medicine"},{"key":"ref_3","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/S0022-3476(70)80038-5","article-title":"Clinical assessment of gestational age in the newborn infant","volume":"77","author":"Dubowitz, L.M.S.; Dubowitz, V.; Goldberg, C.","year":"1970","unstructured":"Dubowitz, L. M. S., Dubowitz, V., and Goldberg, C. (1970). Clinical assessment of gestational age in the newborn infant. Journal of Pediatrics, 77, 1-10.","journal-title":"Journal of Pediatrics"},{"key":"ref_4","doi-asserted-by":"crossref","first-page":"152","DOI":"10.1136\/adc.48.2.152","article-title":"Clinical assessment of gestational age in the neonate","volume":"48","author":"Hancock, B.W.","year":"1973","unstructured":"Hancock, B. W. (1973). Clinical assessment of gestational age in the neonate. Archives of Disease in Childhood, 48, 152-154.","journal-title":"Archives of Disease in Childhood"},{"key":"ref_5","first-page":"2123","article-title":"Clinical assessment of gestational age in the newborn","volume":"47","author":"Jaroszewicz, A.M.; Boyd, I.H.","year":"1973","unstructured":"Jaroszewicz, A. M., and Boyd, I. H. (1973). Clinical assessment of gestational age in the newborn. South African Medical Journal, 47, 2123-2124.","journal-title":"South African Medical Journal"},{"key":"ref_6","first-page":"568","article-title":"Intra-uterine growth standards of Cape Coloured babies. (In Afrikaans)","volume":"49","author":"Jaroszewicz, A.M.; Schumann, D.E.; Keet, M.P.","year":"1975","unstructured":"Jaroszewicz, A. M., Schumann, D. E., and Keet, M. P. (1975). Intra-uterine growth standards of Cape Coloured babies. (In Afrikaans). South African Medical Journal, 49, 568-572.","journal-title":"South African Medical Journal"},{"key":"ref_7","doi-asserted-by":"crossref","first-page":"477","DOI":"10.1001\/archpedi.1976.02120060023005","article-title":"Estimation of gestational age in the neonate","volume":"130","author":"Nicolopoulos, D.; Perakis, A.; Papodakis, M.; Alexion, D.; Aravantinas, D.","year":"1976","unstructured":"Nicolopoulos, D., Perakis, A., Papodakis, M., Alexion, D., and Aravantinas, D. (1976). Estimation of gestational age in the neonate. American Journal of Diseases of Children, 130, 477-480.","journal-title":"American Journal of Diseases of Children"},{"key":"ref_8","doi-asserted-by":"crossref","first-page":"259","DOI":"10.1136\/adc.51.4.259","article-title":"Rapid assessment of gestational age at birth","volume":"51","author":"Parkin, J.M.; Hey, E.N.; Clowes, J.S.","year":"1976","unstructured":"Parkin, J. M., Hey, E. N., and Clowes, J. S. (1976). Rapid assessment of gestational age at birth. Archives of Disease in Childhood, 51, 259-263.","journal-title":"Archives of Disease in Childhood"},{"key":"ref_9","doi-asserted-by":"crossref","first-page":"437","DOI":"10.1136\/adc.41.218.437","article-title":"Assessment of gestational age by neurological examination","volume":"41","author":"Robinson, R.J.","year":"1966","unstructured":"Robinson, R. J. (1966). Assessment of gestational age by neurological examination. Archives ofDisease in Childhood, 41, 437-447.","journal-title":"Archives ofDisease in Childhood"},{"key":"ref_10","article-title":"defined the diencephalic syndrome, a number of reports have described the wide spectrum of symptoms. In this report we call attention to the possible role of catecholamines in producing some of the symptoms","author":"Russell, Since","year":"1951","unstructured":"Since Russell (1951) defined the diencephalic syndrome, a number of reports have described the wide spectrum of symptoms. In this report we call attention to the possible role of catecholamines in producing some of the symptoms."},{"key":"ref_11","article-title":"eliminated in 24-hour urine samples of healthy Greek children, aged from 3 to 12 years, are 14 5 \u00b1 6-3, ug and 4 9 \u00b1 2-3, ug respectively in our laboratory, by the fluorometric method of Crout (1961), on specimens purified by aluminium oxide column chromatography","unstructured":"eliminated in 24-hour urine samples of healthy Greek children, aged from 3 to 12 years, are 14 5 \u00b1 6-3,ug and 4 9 \u00b1 2-3,ug respectively in our laboratory, by the fluorometric method of Crout (1961), on specimens purified by aluminium oxide column chromatography."},{"key":"ref_12","article-title":"Our case presents the usual symptoms and laboratory findings of a diencephalic syndrome, associated with a space-occupying lesion, probably a tumour, situated in the anterior hypothalamus, which is pressing and distorting the 3rd ventricle. Interesting features are (a) moderately raised blood pressure compared with healthy children studied by Lieberman (1974), and (b) a huge increase of urinary (E) and (N)","author":"et al.,","year":"1951","unstructured":"Our case presents the usual symptoms and laboratory findings of a diencephalic syndrome, associated with a space-occupying lesion, probably a tumour, situated in the anterior hypothalamus, which is pressing and distorting the 3rd ventricle. Interesting features are (a) moderately raised blood pressure compared with healthy children studied by Lieberman (1974), and (b) a huge increase of urinary (E) and (N). Since Russell (1951) defined this syndrome a wide spectrum of clinical manifestations (Burr et al., 1976) and a variety of lesion sites in the diencephalon (Addy and Hudson, 1972) have been described.","journal-title":"Since Russell; defined this syndrome a wide spectrum of clinical manifestations (Burr"},{"key":"ref_13","article-title":"This syndrome is one in which several apparently unrelated symptoms, i.e. marasmus, lipodystrophy, and nystagmus, together with various abnormalities of the autonomic nervous system, are attributed to a solitary lesion in the diencephalon. This lesion affects both thalamic nuclei and thalamo-hypothalamo-hypophyseal pathways","year":"1966","unstructured":"This syndrome is one in which several apparently unrelated symptoms, i.e. marasmus, lipodystrophy, and nystagmus, together with various abnormalities of the autonomic nervous system, are attributed to a solitary lesion in the diencephalon. This lesion affects both thalamic nuclei and thalamo-hypothalamo-hypophyseal pathways (Bain et al., 1966)."},{"key":"ref_14","article-title":"There have been few attempts to explain symptoms such as euphoria, diarrhoea, vomiting, sweating, and skin pallor in terms of autonomic nervous system dysfunction, as measured by urinary catecholamine levels, perhaps because increased blood pressure has rarely been reported in Russell's diencephalic syndrome. Mild increase of catecholamine secretion has been noticed in many intracranial tumours and attributed to pressure on the corresponding nervous pathways","author":"A","year":"1972","unstructured":"There have been few attempts to explain symptoms such as euphoria, diarrhoea, vomiting, sweating, and skin pallor in terms of autonomic nervous system dysfunction, as measured by urinary catecholamine levels, perhaps because increased blood pressure has rarely been reported in Russell's diencephalic syndrome. Mild increase of catecholamine secretion has been noticed in many intracranial tumours and attributed to pressure on the corresponding nervous pathways. Nevertheless, the observation of Evans et al. (1972) that urinary catecholamines were increased during episodes of hypertension in a case of proven astrocytoma, mimicking clinical features of pheochromocytoma, is indeed challenging. A","journal-title":"Nevertheless, the observation of Evans et al; that urinary catecholamines were increased during episodes of hypertension in a case of proven astrocytoma, mimicking clinical features of pheochromocytoma, is indeed challenging"},{"key":"ref_15","article-title":"Our patient had most of the symptoms attributed to stimulation of the autonomic nervous I-cell disease is an inherited condition clinically system, such as euphoria, irritability, and skin resembling Hurler's disease but without excessive pallor; she also had a mild but constant hyperurinary mucopolysaccharide excretion. In contrast tension (115\/75 \u00b1 5\/5 mmHg)","unstructured":"). Our patient had most of the symptoms attributed to stimulation of the autonomic nervous I-cell disease is an inherited condition clinically system, such as euphoria, irritability, and skin resembling Hurler's disease but without excessive pallor; she also had a mild but constant hyperurinary mucopolysaccharide excretion. In contrast tension (115\/75 \u00b1 5\/5 mmHg)."},{"key":"ref_16","article-title":"infection in infancy or early childhood. Recent work","volume-title":"suggests that the basic defect Summary is a deficit of neuraminidase. A further case is here reported, and the differential diagnosis and patho","year":"1976","unstructured":"infection in infancy or early childhood. Recent work (Strecker et al., 1976) suggests that the basic defect Summary is a deficit of neuraminidase. A further case is here reported, and the differential diagnosis and patho-"},{"key":"ref_17","first-page":"338","article-title":"Diencephalic respiratory tract infections. syndrome of infantile emaciation. Archives of Disease in At age 4 months he was admitted to hospital for","volume":"47","author":"Addy, D.P.; Hudson, F.P.","year":"1972","unstructured":"Addy, D. P., and Hudson, F. P. (1972). Diencephalic respiratory tract infections. syndrome of infantile emaciation. Archives of Disease in At age 4 months he was admitted to hospital for Childhood, 47, 338-343.","journal-title":"Childhood"},{"key":"ref_18","doi-asserted-by":"crossref","first-page":"237","DOI":"10.1056\/NEJM197208032870508","article-title":"Catecholamines","volume":"287","author":"Axelrod, J.; Weinshilboum, R.","year":"1972","unstructured":"Axelrod, J., and Weinshilboum, R. (1972). Catecholamines. New England Journal of Medicine, 287, 237-243.","journal-title":"New England Journal of Medicine"},{"key":"ref_19","doi-asserted-by":"crossref","first-page":"473","DOI":"10.1542\/peds.38.3.473","article-title":"The diencephalic syndrome of early infancy due to silent brain tumor: with special reference to treatment","volume":"38","author":"Bain, H.W.; Darte, J.M.M.; Keith, W.S.; Kruyff, E.","year":"1966","unstructured":"Bain, H. W., Darte, J. M. M., Keith, W. S., and Kruyff, E. (1966). The diencephalic syndrome of early infancy due to silent brain tumor: with special reference to treatment. Pediatrics, 38, 473-482.","journal-title":"Pediatrics"},{"key":"ref_20","first-page":"439","article-title":"Diencephalic syndrome revisited","volume":"88","author":"Butler, I.J.","year":"1976","unstructured":"Butler, I. J. (1976). Diencephalic syndrome revisited. Journal ofPediatrics, 88, 439-444.","journal-title":"Journal ofPediatrics"},{"key":"ref_21","doi-asserted-by":"crossref","first-page":"62","DOI":"10.1016\/B978-1-4831-9684-8.50012-0","article-title":"Catecholamines in urine","author":"Crout, J.R.","year":"1961","unstructured":"Crout, J. R. (1961). Catecholamines in urine. Cited by Seligson, D. Standard Methods of Clinical Chemistry, pp. 62-64. Academic Press, New York.","journal-title":"Standard Methods of Clinical Chemistry"},{"key":"ref_22","first-page":"1397","article-title":"Astrocytoma mimicking features of pheochromocytoma. New a dorsolumbar kyphoscolosis. The liver was enlarged and palpable to 3 cm, the spleen was not palpable. The hands and feet were broad and his thumbs were held enclosed by his first and second fingers. The skin showed varying degrees of thickening particularly over the shoulders and around the England","volume":"286","year":"1972","unstructured":"Evans, C. H., Westfall, V., and Atuk, N. 0. (1972). Astrocytoma mimicking features of pheochromocytoma. New a dorsolumbar kyphoscolosis. The liver was enlarged and palpable to 3 cm, the spleen was not palpable. The hands and feet were broad and his thumbs were held enclosed by his first and second fingers. The skin showed varying degrees of thickening particularly over the shoulders and around the England Journal of Medicine, 286, 1397-1399.","journal-title":"Journal of Medicine"},{"key":"ref_23","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1016\/S0022-3476(74)80276-3","article-title":"Essential hypertension in children and youth: a pediatric perspective","volume":"85","author":"Lieberman, E.","year":"1974","unstructured":"Lieberman, E. (1974). Essential hypertension in children and youth: a pediatric perspective. Journal of Pediatrics, 85, 1-11.","journal-title":"Journal of Pediatrics"},{"key":"ref_24","first-page":"274","article-title":"A diencephalic syndrome of emaciation in infancy and childhood","volume":"26","author":"Russell, A.","year":"1951","unstructured":"Russell, A. (1951). A diencephalic syndrome of emaciation in infancy and childhood. (Abst.) Archives of Disease in Childhood, 26, 274.","journal-title":"(Abst.) 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