{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,29]],"date-time":"2026-07-29T02:43:44Z","timestamp":1785293024174,"version":"3.55.0"},"reference-count":25,"publisher":"Elsevier BV","issue":"2","license":[{"start":{"date-parts":[[2011,2,1]],"date-time":"2011-02-01T00:00:00Z","timestamp":1296518400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"},{"start":{"date-parts":[[2011,2,1]],"date-time":"2011-02-01T00:00:00Z","timestamp":1296518400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/legal\/tdmrep-license"}],"content-domain":{"domain":["ard.eular.org","elsevier.com","sciencedirect.com"],"crossmark-restriction":true},"short-container-title":["Annals of the Rheumatic Diseases"],"published-print":{"date-parts":[[2011,2]]},"DOI":"10.1136\/ard.2010.132613","type":"journal-article","created":{"date-parts":[[2010,11,17]],"date-time":"2010-11-17T01:34:51Z","timestamp":1289957691000},"page":"309-314","update-policy":"https:\/\/doi.org\/10.1016\/elsevier_cm_policy","source":"Crossref","is-referenced-by-count":74,"title":["A preliminary score for the assessment of disease activity in hereditary recurrent fevers: results from the AIDAI (Auto-Inflammatory Diseases Activity Index) Consensus Conference"],"prefix":"10.1016","volume":"70","author":[{"given":"Maryam","family":"Piram","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Joost","family":"Frenkel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marco","family":"Gattorno","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Seza","family":"Ozen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Helen J","family":"Lachmann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Raphaela","family":"Goldbach-Mansky","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"V\u00e9ronique","family":"Hentgen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"B\u00e9n\u00e9dicte","family":"Neven","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Katia Stankovic","family":"Stojanovic","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Anna","family":"Simon","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jasmin","family":"Kuemmerle-Deschner","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hal","family":"Hoffman","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Silvia","family":"Stojanov","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Agn\u00e8s","family":"Duquesne","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pascal","family":"Pillet","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alberto","family":"Martini","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jacques","family":"Pouchot","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Isabelle","family":"Kon\u00e9-Paut","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1136\/ard.2010.132613_bib1","doi-asserted-by":"crossref","first-page":"811","DOI":"10.1016\/j.berh.2008.08.009","article-title":"Autoinflammatory diseases","volume":"22","author":"Touitou","year":"2008","journal-title":"Best Pract Res Clin Rheumatol"},{"key":"10.1136\/ard.2010.132613_bib2","doi-asserted-by":"crossref","first-page":"2416","DOI":"10.1056\/NEJMoa0810787","article-title":"Use of canakinumab in the cryopyrin-associated periodic syndrome","volume":"360","author":"Lachmann","year":"2009","journal-title":"N Engl J Med"},{"key":"10.1136\/ard.2010.132613_bib3","doi-asserted-by":"crossref","first-page":"2443","DOI":"10.1002\/art.23687","article-title":"Efficacy and safety of rilonacept (interleukin-1 Trap) in patients with cryopyrin-associated periodic syndromes: results from two sequential placebo-controlled studies","volume":"58","author":"Hoffman","year":"2008","journal-title":"Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib4","doi-asserted-by":"crossref","first-page":"e96","DOI":"10.1371\/journal.pmed.0050096","article-title":"A systematic review of studies that aim to determine which outcomes to measure in clinical trials in children","volume":"5","author":"Sinha","year":"2008","journal-title":"PLoS Med"},{"key":"10.1136\/ard.2010.132613_bib5","doi-asserted-by":"crossref","first-page":"1748","DOI":"10.1056\/NEJMra010200","article-title":"Hereditary periodic fever","volume":"345","author":"Drenth","year":"2001","journal-title":"N Engl J Med"},{"key":"10.1136\/ard.2010.132613_bib6","doi-asserted-by":"crossref","first-page":"796","DOI":"10.1093\/rheumatology\/keh597","article-title":"What does \u201cactive disease\u201d mean? patient and part5ent perceptions of disease activity in the systemic arthritis form of juvenile idiopathic arthritis (SO-JIA)","volume":"44","author":"Batthish","year":"2005","journal-title":"Rheumatology (Oxford)"},{"key":"10.1136\/ard.2010.132613_bib7","doi-asserted-by":"crossref","first-page":"1452","DOI":"10.1093\/rheumatology\/keg403","article-title":"Preliminary core sets of measures for disease activity and damage assessment in juvenile systemic lupus erythematosus and juvenile dermatomyositis","volume":"42","author":"Ruperto","year":"2003","journal-title":"Rheumatology (Oxford)"},{"key":"10.1136\/ard.2010.132613_bib8","doi-asserted-by":"crossref","first-page":"142","DOI":"10.1007\/s11926-008-0025-6","article-title":"Consensus procedures and their role in pediatric rheumatology","volume":"10","author":"Ruperto","year":"2008","journal-title":"Curr Rheumatol Rep"},{"key":"10.1136\/ard.2010.132613_bib9","doi-asserted-by":"crossref","first-page":"376","DOI":"10.1136\/bmj.311.7001.376","article-title":"Consensus methods for medical and health services research","volume":"311","author":"Jones","year":"1995","journal-title":"BMJ"},{"key":"10.1136\/ard.2010.132613_bib10","doi-asserted-by":"crossref","first-page":"203","DOI":"10.1002\/art.22551","article-title":"The Pediatric Rheumatology European Society\/American College of Rheumatology\/European League against Rheumatism provisional classification criteria for juvenile systemic sclerosis","volume":"57","author":"Zulian","year":"2007","journal-title":"Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib11","doi-asserted-by":"crossref","first-page":"e474","DOI":"10.1542\/peds.2006-1434","article-title":"Colchicine use in children and adolescents with familial Mediterranean fever: literature review and consensus statement","volume":"119","author":"Kallinich","year":"2007","journal-title":"Pediatrics"},{"key":"10.1136\/ard.2010.132613_bib12","doi-asserted-by":"crossref","first-page":"612","DOI":"10.1016\/S0049-0172(96)80012-6","article-title":"The changing face of familial Mediterranean fever","volume":"26","author":"Livneh","year":"1996","journal-title":"Semin Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib13","doi-asserted-by":"crossref","first-page":"1879","DOI":"10.1002\/art.1780401023","article-title":"Criteria for the diagnosis of familial Mediterranean fever","volume":"40","author":"Livneh","year":"1997","journal-title":"Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib14","doi-asserted-by":"crossref","first-page":"108","DOI":"10.1097\/01.bor.0000198006.65697.5b","article-title":"Familial Mediterranean fever and the other autoinflammatory syndromes: evaluation of the patient with recurrent fever","volume":"18","author":"Samuels","year":"2006","journal-title":"Curr Opin Rheumatol"},{"key":"10.1136\/ard.2010.132613_bib15","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1097\/01.md.0000152370.84628.0c","article-title":"Familial Mediterranean fever (FMF) in Turkey: results of a nationwide multicenter study","volume":"84","author":"Tunca","year":"2005","journal-title":"Medicine (Baltimore)"},{"key":"10.1136\/ard.2010.132613_bib16","doi-asserted-by":"crossref","first-page":"395","DOI":"10.1093\/rheumatology\/ken509","article-title":"A new set of criteria for the diagnosis of familial Mediterranean fever in childhood","volume":"48","author":"Yal\u00e7inkaya","year":"2009","journal-title":"Rheumatology (Oxford)"},{"key":"10.1136\/ard.2010.132613_bib17","doi-asserted-by":"crossref","first-page":"301","DOI":"10.1097\/MD.0b013e318190cfb7","article-title":"Long-term follow-up, clinical features, and quality of life in a series of 103 patients with hyperimmunoglobulinemia D syndrome","volume":"87","author":"van der Hilst","year":"2008","journal-title":"Medicine (Baltimore)"},{"key":"10.1136\/ard.2010.132613_bib18","doi-asserted-by":"crossref","first-page":"2181","DOI":"10.1002\/art.10429","article-title":"The enlarging clinical, genetic, and population spectrum of tumor necrosis factor receptor-associated periodic syndrome","volume":"46","author":"Dod\u00e9","year":"2002","journal-title":"Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib19","doi-asserted-by":"crossref","first-page":"1273","DOI":"10.1002\/art.22491","article-title":"The clinical continuum of cryopyrinopathies: novel CIAS1 mutations in North American patients and a new cryopyrin model","volume":"56","author":"Aksentijevich","year":"2007","journal-title":"Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib20","doi-asserted-by":"crossref","first-page":"348","DOI":"10.1002\/art.22003","article-title":"Development of classification and response criteria for rheumatic diseases","volume":"55","author":"Singh","year":"2006","journal-title":"Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib21","doi-asserted-by":"crossref","first-page":"658","DOI":"10.1002\/art.24516","article-title":"Development and validation of a composite disease activity score for juvenile idiopathic arthritis","volume":"61","author":"Consolaro","year":"2009","journal-title":"Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib22","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1016\/j.semarthrit.2005.02.002","article-title":"Evaluation of disease severity in familial Mediterranean fever","volume":"35","author":"Mor","year":"2005","journal-title":"Semin Arthritis Rheum"},{"key":"10.1136\/ard.2010.132613_bib23","doi-asserted-by":"crossref","first-page":"216","DOI":"10.1002\/(SICI)1096-8628(19980113)75:2<216::AID-AJMG20>3.0.CO;2-R","article-title":"Clinical differences between North African and Iraqi Jews with familial Mediterranean fever","volume":"75","author":"Pras","year":"1998","journal-title":"Am J Med Genet"},{"key":"10.1136\/ard.2010.132613_bib24","doi-asserted-by":"crossref","first-page":"246","DOI":"10.1136\/ard.2008.092031","article-title":"Disease severity in children and adolescents with familial Mediterranean fever: a comparative study to explore environmental effects on a monogenic disease","volume":"68","author":"Ozen","year":"2009","journal-title":"Ann Rheum Dis"},{"key":"10.1136\/ard.2010.132613_bib25","doi-asserted-by":"crossref","first-page":"24","DOI":"10.1016\/S0140-6736(00)05252-1","article-title":"Amyloid load and clinical outcome in AA amyloidosis in relation to circulating concentration of serum amyloid A protein","volume":"358","author":"Gillmore","year":"2001","journal-title":"Lancet"}],"container-title":["Annals of the Rheumatic Diseases"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0003496724146778?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0003496724146778?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/ard.2010.132613","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,1,20]],"date-time":"2025-01-20T05:04:43Z","timestamp":1737349483000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0003496724146778"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,2]]},"references-count":25,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2011,2]]}},"alternative-id":["S0003496724146778"],"URL":"https:\/\/doi.org\/10.1136\/ard.2010.132613","relation":{},"ISSN":["0003-4967"],"issn-type":[{"value":"0003-4967","type":"print"}],"subject":[],"published":{"date-parts":[[2011,2]]},"assertion":[{"value":"Elsevier","name":"publisher","label":"This article is maintained by"},{"value":"A preliminary score for the assessment of disease activity in hereditary recurrent fevers: results from the AIDAI (Auto-Inflammatory Diseases Activity Index) Consensus Conference","name":"articletitle","label":"Article Title"},{"value":"Annals of the Rheumatic Diseases","name":"journaltitle","label":"Journal Title"},{"value":"https:\/\/doi.org\/10.1136\/ard.2010.132613","name":"articlelink","label":"CrossRef DOI link to publisher maintained version"},{"value":"article","name":"content_type","label":"Content Type"},{"value":"Copyright \u00a9 2011 Published by Elsevier Inc. For permission to use (where not already granted under a licence) please go to http:\/\/group.bmj.com\/group\/rights-licensing\/permissions. Published by Elsevier B.V. All rights are reserved, including those for text and data mining, AI training, and similar technologies.","name":"copyright","label":"Copyright"}]}}