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We report a case of a 13-year-old Chilean girl who presented with an 8-month history of progressive exercise intolerance, fatigability and diminished school performance. Physical examination revealed resting tachypnoea, a few basal bilateral inspiratory crackles, and hypoxaemia on minimal exertion. Clinical suspicion and evaluation, including international collaboration, led to the diagnosis of autoimmune PAP and specific therapy for the condition.<\/jats:p>","DOI":"10.1136\/bcr-2012-006987","type":"journal-article","created":{"date-parts":[[2014,5,23]],"date-time":"2014-05-23T10:32:29Z","timestamp":1400841149000},"page":"bcr2012006987","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Autoimmune pulmonary proteinosis in a Chilean teenager, a rare aetiology of interstitial lung disease"],"prefix":"10.1136","volume":"2014","author":[{"given":"Alexis","family":"Strickler","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Maria 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