{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T09:40:09Z","timestamp":1756374009044,"version":"3.44.0"},"reference-count":86,"publisher":"BMJ","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Reports"],"abstract":"<jats:p>The Mucha-Habermann disease is an inflammatory disease of the skin and is a variant of pityriasis lichenoides et varioliformis acuta. We describe the case of a 64-years-old woman who was admitted for erysipelas of the face. Despite treatment, evolution was marked by the appearance of a necrotising ulcerative area in the centre of the erysipelas associated with local oedema and headache. A skin biopsy revealed a pityriasis lichenoides et varioliformis acuta. Corticosteroids led to a rapid stabilisation of lesions, and after 6\u2005months the patient shows only a small area of frontal hypopigmentation. The aetiology remains uncertain. There is no established standard treatment. We would like to draw attention of the medical and surgical specialists to this rare disease. The diagnosis should be considered in a necrotic lesion associated with rapid expansion of systemic and peripheral cutaneous signs. Diagnosis must be considered to avoid unnecessary debridement and extensive scars.<\/jats:p>","DOI":"10.1136\/bcr-2013-009739","type":"journal-article","created":{"date-parts":[[2013,10,14]],"date-time":"2013-10-14T06:13:28Z","timestamp":1381731208000},"page":"bcr2013009739","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":5,"title":["Febrile ulceronecrotic Mucha-Habermann disease"],"prefix":"10.1136","volume":"2013","author":[{"given":"F-X","family":"Lejuste","sequence":"first","affiliation":[{"name":"Service de Chirurgie Plastique Reconstructrice et Esth\u00e9tique, Centre Hospitalier de Luxembourg, Luxembourg, Luxembourg"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C","family":"Michaux","sequence":"additional","affiliation":[{"name":"Service des Maladies Infectieuses, Centre Hospitalier de Luxembourg, Luxembourg, Luxembourg"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C","family":"Lehners","sequence":"additional","affiliation":[{"name":"Service de Dermatologie, Centre Hospitalier de Luxembourg, Luxembourg, Luxembourg"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"N","family":"Calteux","sequence":"additional","affiliation":[{"name":"Service de Chirurgie Plastique Reconstructrice et Esth\u00e9tique, Centre Hospitalier de Luxembourg, Luxembourg, Luxembourg"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2013,10,14]]},"reference":[{"key":"2025082802074613000_2013.oct14_1.bcr2013009739.1","doi-asserted-by":"crossref","first-page":"78","DOI":"10.1016\/j.anplas.2008.12.001","article-title":"Necrotizing fasciitis after a blunt trauma","volume":"2013","author":"Raffoul","year":"2010","journal-title":"Ann Chir Plast Esthet"},{"key":"2025082802074613000_2013.oct14_1.bcr2013009739.2","doi-asserted-by":"crossref","first-page":"123","DOI":"10.1016\/j.anplas.2010.10.001","article-title":"[Necrotizing fasciitis: study of 17 cases presenting a low mortality rate]","volume":"2013","author":"Kibadi","year":"2013;","journal-title":"Ann Chir Plast Esthet"},{"key":"2025082802074613000_2013.oct14_1.bcr2013009739.3","doi-asserted-by":"crossref","first-page":"1689","DOI":"10.1056\/NEJM198406283102601","article-title":"Early recognition of potentially fatal necrotizing fasciitis. 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