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We report a young girl with primary CAPS who presented with pulmonary hypertension and an inferior vena cava mass masquerading as a tumour.<\/jats:p>","DOI":"10.1136\/bcr-2013-010043","type":"journal-article","created":{"date-parts":[[2013,7,16]],"date-time":"2013-07-16T08:34:11Z","timestamp":1373963651000},"page":"bcr2013010043","source":"Crossref","is-referenced-by-count":1,"title":["Catastrophic antiphospholipid syndrome in childhood: presentation with an inferior caval vein mass"],"prefix":"10.1136","volume":"2013","author":[{"given":"Abdul Alim","family":"Abdul Haium","sequence":"first","affiliation":[{"name":"Department of Paediatric Cardiology, Royal Brompton Hospital, London, UK"},{"name":"Department of Neonatology, K K Women's and Children's Hospital, Singapore"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mary","family":"Sheppard","sequence":"additional","affiliation":[{"name":"Department of Pathology, Royal Brompton Hospital, London, UK"},{"name":"National Heart Lung Institute, Imperial College, London, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Michael","family":"Rubens","sequence":"additional","affiliation":[{"name":"Department of Radiology, Royal Brompton Hospital, London, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Piers","family":"Daubeney","sequence":"additional","affiliation":[{"name":"Department of Paediatric Cardiology, Royal Brompton Hospital, London, UK"},{"name":"National Heart Lung Institute, Imperial College, London, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2013,7,16]]},"reference":[{"key":"2025082804010461000_2013.jul16_1.bcr2013010043.1","doi-asserted-by":"crossref","first-page":"1019","DOI":"10.1002\/art.10187","article-title":"Antiphospholipid syndrome: clinical and immunologic manifestations and patterns of disease expression in a cohort of 1,000 patients","volume":"2013","author":"Cervera","year":"2002","journal-title":"Arthritis Rheum"},{"key":"2025082804010461000_2013.jul16_1.bcr2013010043.2","first-page":"508","article-title":"The catastrophic antiphospholipid syndrome","volume-title":"J Rheumatol","volume":"2013","author":"Asherson","year":"1992"},{"key":"2025082804010461000_2013.jul16_1.bcr2013010043.3","doi-asserted-by":"crossref","first-page":"530","DOI":"10.1191\/0961203303lu394oa","article-title":"Catastrophic antiphospholipid syndrome: international consensus statement on classification criteria and treatment guidelines","volume":"2013","author":"Asherson","year":"2003","journal-title":"Lupus"},{"key":"2025082804010461000_2013.jul16_1.bcr2013010043.4","doi-asserted-by":"crossref","first-page":"195","DOI":"10.1097\/00005792-199805000-00005","article-title":"Catastrophic antibody syndrome. 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