{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,4,27]],"date-time":"2025-04-27T09:40:02Z","timestamp":1745746802032,"version":"3.40.4"},"reference-count":16,"publisher":"BMJ","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Reports"],"abstract":"<jats:p>A 49-year-old woman presented with occipital headaches, dizziness, photophobia and vomiting for 2\u2005weeks\u2019 status post posterior scalp mole removal by a general surgeon. The physical examination revealed occipital lesions with foul smelling purulent discharge mixed with clear fluid drainage, webbed neck with decreased range of motion, facial asymmetry and a low posterior hairline. A CT of head showed occipital skull defect providing a communicating pathway for scalp infection, an atlas fusion defect and an extensive pneumoencephaly. Further imaging showed low-lying cerebellar tonsils and fusion of the body of second and third cervical vertebrae. Klippel-Feil syndrome was diagnosed and the patient was successfully managed with duraplasty of occipital dura, placement of a lumbar drain and antibiotics. In patients with findings suggestive of Klippel-Feil syndrome and lesions proximal to the CNS, appropriate neuroimaging and possible neurosurgical consult should be considered prior to any surgical intervention.<\/jats:p>","DOI":"10.1136\/bcr-2013-201234","type":"journal-article","created":{"date-parts":[[2014,1,15]],"date-time":"2014-01-15T14:59:23Z","timestamp":1389797963000},"page":"bcr2013201234","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Postsurgical pneumoencephaly in a patient with Klippel-Feil syndrome"],"prefix":"10.1136","volume":"2014","author":[{"given":"Nasir","family":"Hussain","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pavani","family":"Thotakura","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Roger A","family":"Lichtenbaum","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Aibek E","family":"Mirrakhimov","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2014,1,15]]},"reference":[{"key":"2025042702134256000_2014.jan15_2.bcr2013201234.1","doi-asserted-by":"publisher","DOI":"10.1097\/01.blo.0000130267.49895.20"},{"key":"2025042702134256000_2014.jan15_2.bcr2013201234.2","doi-asserted-by":"publisher","DOI":"10.1016\/S0140-6736(03)12987-X"},{"key":"2025042702134256000_2014.jan15_2.bcr2013201234.3","doi-asserted-by":"publisher","DOI":"10.2174\/138920111795542615"},{"key":"2025042702134256000_2014.jan15_2.bcr2013201234.4","doi-asserted-by":"publisher","DOI":"10.1016\/j.ecl.2012.08.007"},{"key":"2025042702134256000_2014.jan15_2.bcr2013201234.5","doi-asserted-by":"publisher","DOI":"10.1016\/S0140-6736(12)61023-X"},{"key":"2025042702134256000_2014.jan15_2.bcr2013201234.6","unstructured":"Jones KL . 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