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These patients develop end-stage renal disease at an earlier age and have an increased risk of malignancy. We present a case of a 30-year-old man with a history of tuberous sclerosis, presenting with loin pain and subsequently diagnosed to have ADPKD.<\/jats:p>","DOI":"10.1136\/bcr-2014-207471","type":"journal-article","created":{"date-parts":[[2014,12,17]],"date-time":"2014-12-17T10:53:20Z","timestamp":1418813600000},"page":"bcr2014207471","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":13,"title":["Tuberous sclerosis complex with autosomal dominant polycystic kidney disease: a rare duo"],"prefix":"10.1136","volume":"2014","author":[{"given":"Jharendra P","family":"Rijal","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Prajwal","family":"Dhakal","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Smith","family":"Giri","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Khagendra 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