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We report on our experience of an infant with ARPKD requiring neonatal renal replacement therapy and survival at 14\u2005months following early bilateral nephrectomy.<\/jats:p>","DOI":"10.1136\/bcr-2015-211106","type":"journal-article","created":{"date-parts":[[2015,12,15]],"date-time":"2015-12-15T12:57:57Z","timestamp":1450184277000},"page":"bcr2015211106","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":8,"title":["Early bilateral nephrectomy in infantile autosomal recessive polycystic kidney disease"],"prefix":"10.1136","volume":"2015","author":[{"given":"Tamara Mary","family":"Mallett","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Emma","family":"O'Hagan","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Karl Gerard","family":"McKeever","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2015,12,15]]},"reference":[{"key":"2025042707493318000_2015.dec15_1.bcr2015211106.1","doi-asserted-by":"publisher","DOI":"10.1002\/(SICI)1096-8628(19980305)76:2<137::AID-AJMG6>3.0.CO;2-Q"},{"key":"2025042707493318000_2015.dec15_1.bcr2015211106.2","doi-asserted-by":"publisher","DOI":"10.1007\/s00467-010-1656-1"},{"key":"2025042707493318000_2015.dec15_1.bcr2015211106.3","doi-asserted-by":"publisher","DOI":"10.1542\/peds.111.5.1072"},{"key":"2025042707493318000_2015.dec15_1.bcr2015211106.4","doi-asserted-by":"publisher","DOI":"10.1111\/j.1399-3046.2006.00644.x"},{"key":"2025042707493318000_2015.dec15_1.bcr2015211106.5","doi-asserted-by":"crossref","unstructured":"Guay-Woodford L . 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