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Immunological remission was achieved after a number of courses of pulsed intravenous methylprednisolone and cyclophosphamide. The patient has remained in remission for 5\u2005years, but has required regular dilation of esophageal strictures for symptom relief. During this period, a chronic lymphocytosis was incidentally noted on routine blood tests, and chronic lymphocytic leukaemia was diagnosed. It is essential to investigate PPI-resistant symptoms, dysphagia and odynophagia, as they may indicate a serious underlying cause.<\/jats:p>","DOI":"10.1136\/bcr-2015-212661","type":"journal-article","created":{"date-parts":[[2015,10,23]],"date-time":"2015-10-23T12:17:47Z","timestamp":1445602667000},"page":"bcr2015212661","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":10,"title":["Pemphigus vulgaris: a rare cause of dysphagia"],"prefix":"10.1136","volume":"2015","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-2094-0556","authenticated-orcid":false,"given":"Ali","family":"Al-Janabi","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Simon","family":"Greenfield","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2015,10,22]]},"reference":[{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.1","doi-asserted-by":"publisher","DOI":"10.1016\/S0190-9622(82)70111-2"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.2","doi-asserted-by":"publisher","DOI":"10.1016\/S0016-5107(04)01605-0"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.3","doi-asserted-by":"publisher","DOI":"10.1055\/s-2002-32124"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.4","doi-asserted-by":"publisher","DOI":"10.1111\/j.1572-0241.2003.07183.x"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.5","doi-asserted-by":"publisher","DOI":"10.1111\/j.1442-2050.2005.00526.x"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.6","first-page":"71","article-title":"Esophageal pemphigus vulgaris: a rare manifestation revisited","volume":"4","author":"Khamaysi","year":"2008","journal-title":"Gastroenterol Hepatol"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.7","first-page":"68","article-title":"An unusual presentation of pemphigus vulgaris","volume":"4","author":"Houghton","year":"2008","journal-title":"Gastroenterol Hepatol"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.8","doi-asserted-by":"publisher","DOI":"10.1016\/0190-9622(91)70031-V"},{"key":"2025042707281184000_2015.oct22_1.bcr2015212661.9","unstructured":"Greenwald DA , Brandt LJ . 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