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Optimum management and pregnancy outcomes in mother with uncorrected Pentalogy of Fallot and twin pregnancy have not been described in the literature. We describe a successful case of monochorionic diamniotic twin pregnancy in an affected woman who has not undergone surgical repair. Her pregnancy progressed without any adverse cardiopulmonary complications. Her caesarean delivery and postpartum recovery were favourable, with successful birth of two healthy babies at 35.7\u2005weeks. This case emphasises the importance of a multidisciplinary team, especially of obstetricians with expertise in high-risk pregnancies, adult congenital heart disease cardiologists and anaesthesiologist.<\/jats:p>","DOI":"10.1136\/bcr-2016-216809","type":"journal-article","created":{"date-parts":[[2017,1,18]],"date-time":"2017-01-18T15:56:12Z","timestamp":1484754972000},"page":"bcr2016216809","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":5,"title":["Multiple pregnancy in a primigravida with uncorrected Pentalogy of Fallot"],"prefix":"10.1136","volume":"2017","author":[{"given":"Pamela","family":"Partana","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jarrod Kah Hwee","family":"Tan","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ju Le","family":"Tan","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lay Kok","family":"Tan","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2017,1,18]]},"reference":[{"key":"2025042702292198000_2017.jan18_1.bcr2016216809.1","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9149(78)90941-4"},{"key":"2025042702292198000_2017.jan18_1.bcr2016216809.2","doi-asserted-by":"crossref","first-page":"631","DOI":"10.1111\/j.0742-2822.2004.03160.x","article-title":"Survival to the age of 52 years in a man with unprepared tetralogy of Fallot","volume":"21","author":"Makaryus","year":"2004","journal-title":"Echocardiography"},{"key":"2025042702292198000_2017.jan18_1.bcr2016216809.3","unstructured":"Zipes DP , Braunwald E . 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