{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,7]],"date-time":"2025-11-07T09:16:23Z","timestamp":1762506983903,"version":"3.44.0"},"reference-count":17,"publisher":"BMJ","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Reports"],"accepted":{"date-parts":[[2016,12,2]]},"abstract":"<jats:p>Sturge-Weber syndrome (SWS) is a rare neurocutaneous syndrome characterised by facial naevus and leptomeningeal angiomatosis resulting in neurological and ophthalmological complications. In its rare variant, SWS type 3, the clinical hallmark of facial naevus is absent which poses a diagnostic challenge. Here, we present an interesting case of SWS type 3 where a child presented twice with prolonged severe unilateral headache mimicking migraine status followed on both occasions with focal seizures. He developed a dense right-sided homonymous hemianopia, and an urgent brain MRI scan was performed which pointed towards the diagnosis of SWS type 3.<\/jats:p>","DOI":"10.1136\/bcr-2016-216842","type":"journal-article","created":{"date-parts":[[2016,12,24]],"date-time":"2016-12-24T13:37:02Z","timestamp":1482586622000},"page":"bcr2016216842","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":9,"title":["Sturge-Weber syndrome type 3 manifesting as \u2018Status migrainosus\u2019"],"prefix":"10.1136","volume":"2016","author":[{"given":"Philip Richard","family":"Jordan","sequence":"first","affiliation":[{"name":"Department of Paediatrics, University Hospitals of Leicester NHS Trust, Leicester, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mehtab","family":"Iqbal","sequence":"additional","affiliation":[{"name":"Department of Paediatric Neurology, University Hospital of Leicester NHS Trust, Leicester, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Manish","family":"Prasad","sequence":"additional","affiliation":[{"name":"Department of Paediatrics, Nottingham University Hospitals Trust, Nottingham, UK"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2016,12,19]]},"reference":[{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa1213507"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.2","doi-asserted-by":"crossref","unstructured":"Hobson C , Foyaca-Sibat H , Hobson B , et al . Sturge Weber Syndrome type 1 \u2018plus\u2019: a case report. Internet J Neurol 2005;5 .","DOI":"10.5580\/c09"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.3","first-page":"23","article-title":"Sturge Weber syndrome type III\u2013a rare case report","volume":"1","author":"Mammen","year":"2015","journal-title":"IOSR J Dent Med Sci"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.4","doi-asserted-by":"crossref","unstructured":"Knipe H , Gaillard F , et al . Sturge-Weber syndrome.rID: 8210 2010. http:\/\/radiopaedia.org\/articles\/sturge-webersyndrome-1 (accessed 13 Apr. 2016).","DOI":"10.53347\/rID-8209"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.5","unstructured":"IHS\u2014International Headache Society. 2016. http:\/\/www.ihs-classification.org\/en\/"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.6","doi-asserted-by":"crossref","first-page":"39","DOI":"10.4103\/1817-1745.131483","article-title":"Paroxysmal vascular events in Sturge\u2013Weber syndrome: role of aspirin","volume":"9","author":"Sanghvi","year":"2014","journal-title":"J Pediatric Neurosci"},{"issue":"(Suppl)","key":"2025082707355664000_2016.dec19_1.bcr2016216842.7","first-page":"293","article-title":"Sturge-Weber syndrome: natural history and prognosis","volume":"3","author":"Rochkind","year":"1990","journal-title":"J Epilepsy"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.8","doi-asserted-by":"crossref","unstructured":"Gomez MR , Bebin EM . Sturge-Weber syndrome. In: Gomez MR, ed . Neurocutaneous diseases: a practical approach. London: Butterworths, 1987:356\u201367.","DOI":"10.1016\/B978-0-409-90018-7.50045-1"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.9","doi-asserted-by":"publisher","DOI":"10.1111\/j.1468-2982.2004.00784.x"},{"issue":"1","key":"2025082707355664000_2016.dec19_1.bcr2016216842.10","doi-asserted-by":"crossref","first-page":"C52","DOI":"10.1186\/1129-2377-15-S1-C52","article-title":"EHMTI-0310. Headache in children with Sturge-Weber syndrome","volume":"15","author":"Prabhakar","year":"2014","journal-title":"J Headache Pain"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.11","doi-asserted-by":"publisher","DOI":"10.1111\/head.12067"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.12","doi-asserted-by":"crossref","first-page":"681","DOI":"10.1016\/j.braindev.2009.09.002","article-title":"Prolonged left homonymous hemianopsia associated with migraine-like attacks in a child with Sturge-Weber Syndrome","volume":"32","author":"Shimakawa","year":"2010","journal-title":"Brain Dev"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.13","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320570110"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.14","doi-asserted-by":"publisher","DOI":"10.1177\/0883073810388646"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.15","doi-asserted-by":"publisher","DOI":"10.1177\/0883073812463607"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.16","doi-asserted-by":"publisher","DOI":"10.1177\/088307389501000113"},{"key":"2025082707355664000_2016.dec19_1.bcr2016216842.17","doi-asserted-by":"crossref","first-page":"722","DOI":"10.1177\/0883073812451326","article-title":"Sturge-Weber syndrome clinical spectrum, disease course, and outcome of 30 patients","volume":"28","author":"Jagtap","year":"2013","journal-title":"J Child Neurol"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2016-216842","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,27]],"date-time":"2025-08-27T14:36:04Z","timestamp":1756305364000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2016-216842"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,12,19]]},"references-count":17,"alternative-id":["10.1136\/bcr-2016-216842"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2016-216842","relation":{},"ISSN":["1757-790X"],"issn-type":[{"type":"electronic","value":"1757-790X"}],"subject":[],"published":{"date-parts":[[2016,12,19]]}}}