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Despite delivery of the fetus, her condition deteriorated over 3\u20134 days with high-grade fever, worsening thrombocytopenia and anaemia requiring transfusion support. A bone marrow biopsy showed haemophagocytosis and a diagnosis of HLH was made. Partial remission was achieved with etoposide-based chemotherapy and complete remission following bone marrow transplantation. Eleven months post-transplant, the disease aggressively recurred, and the patient died within 3\u2009weeks of relapse.<\/jats:p>","DOI":"10.1136\/bcr-2017-219516","type":"journal-article","created":{"date-parts":[[2017,4,22]],"date-time":"2017-04-22T05:00:16Z","timestamp":1492837216000},"page":"bcr-2017-219516","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":14,"title":["Haemophagocytic lymphohistiocytosis presenting as HELLP syndrome: a diagnostic and therapeutic challenge"],"prefix":"10.1136","volume":"2017","author":[{"given":"Robert Noel","family":"Kerley","sequence":"first","affiliation":[{"name":"University College Cork, National University of Ireland, Cork, Ireland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Raymond Michael","family":"Kelly","sequence":"additional","affiliation":[{"name":"University College Cork, National University of Ireland, Cork, 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