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Although the patient had Behcet\u2019s disease (BD)-like symptoms, pancytopenia could not be explained by the diagnosis, prompting a bone marrow biopsy which showed myelodysplastic syndrome. This report highlights the importance of excluding alternate disorders before making a diagnosis of Behcet\u2019s disease if atypical, BD-incompatible or incomplete constellations of symptoms and findings are present.<\/jats:p>","DOI":"10.1136\/bcr-2017-220649","type":"journal-article","created":{"date-parts":[[2018,3,15]],"date-time":"2018-03-15T09:30:29Z","timestamp":1521106229000},"page":"bcr-2017-220649","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":4,"title":["Myelodysplastic syndrome presenting as a Beh\u00e7et\u2019s-like disease with aortitis"],"prefix":"10.1136","volume":"2018","author":[{"given":"Shudan","family":"Wang","sequence":"first","affiliation":[{"name":"Division of Rheumatology, Department of Medicine, NYU School of Medicine, New York, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Noam","family":"Broder","sequence":"additional","affiliation":[{"name":"Department of Medicine, NYU School of Medicine, New York, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Paula","family":"Marchetta","sequence":"additional","affiliation":[{"name":"Division of Rheumatology, Department of Medicine, NYU School of Medicine, New York, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Johannes","family":"Nowatzky","sequence":"additional","affiliation":[{"name":"Division of Rheumatology, Department of Medicine, NYU School of Medicine, New York, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2018,3,15]]},"reference":[{"key":"2025082707081280000_2018.mar15_1.bcr-2017-220649.1","first-page":"1078","article-title":"Criteria for diagnosis of Beh\u00e7et\u2019s disease","volume":"335","author":"International Study Group for Beh\u00e7et\u2019s Disease","year":"1990","journal-title":"Lancet"},{"key":"2025082707081280000_2018.mar15_1.bcr-2017-220649.2","doi-asserted-by":"publisher","DOI":"10.1016\/j.leukres.2013.04.007"},{"key":"2025082707081280000_2018.mar15_1.bcr-2017-220649.3","unstructured":"Hamblin TJ . 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