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A positron emission tomography (PET)-CT detected multiple adenopathies. Cytology revealed adenocarcinoma with an immunocytology compatible with a breast origin and this was considered as a late metastatic recurrence of her previous breast cancer. A treatment of prednisone, dapsone and hormonotherapy was introduced, but intravenous immunoglobulin and rituximab were added due to new mucosal lesions. Despite treatment, a posterior laryngeal scar and bilateral symblepharon were developed. After 3 years, the patient is still alive and reports a satisfactory quality of life.<\/jats:p>","DOI":"10.1136\/bcr-2017-220887","type":"journal-article","created":{"date-parts":[[2017,8,11]],"date-time":"2017-08-11T15:20:17Z","timestamp":1502464817000},"page":"bcr-2017-220887","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":15,"title":["Paraneoplastic mucous membrane pemphigoid with ocular and laryngeal 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