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Special considerations were made with regard to muscle relaxation given the complications associated with inadequate paralysis and reversal in patients with HD. The technique we describe may also apply to other patient categories, such as patients with movement disorders, bulbar dysfunction and dementia.<\/jats:p>","DOI":"10.1136\/bcr-2017-221354","type":"journal-article","created":{"date-parts":[[2017,10,20]],"date-time":"2017-10-20T00:15:20Z","timestamp":1508458520000},"page":"bcr-2017-221354","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":5,"title":["Anaesthesia and orphan disease: airway and anaesthetic management in Huntington\u2019s disease"],"prefix":"10.1136","volume":"2017","author":[{"given":"Phuong Thao","family":"Nguyen","sequence":"first","affiliation":[{"name":"Department of Anaesthesia, Brighton and Sussex University Hospitals NHS Trust, Brighton, UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Daveena","family":"Meeks","sequence":"additional","affiliation":[{"name":"Department of Anaesthesia, Brighton and Sussex University Hospitals NHS Trust, Brighton, UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Despoina","family":"Liotiri","sequence":"additional","affiliation":[{"name":"Department of Anaesthesia, Brighton and Sussex University Hospitals NHS Trust, Brighton, UK"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2017,10,19]]},"reference":[{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.1","doi-asserted-by":"publisher","DOI":"10.1186\/1750-1172-5-40"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.2","doi-asserted-by":"crossref","first-page":"15005","DOI":"10.1038\/nrdp.2015.5","article-title":"Huntington disease","volume":"26","author":"Bates","year":"2015","journal-title":"Nat Rev Dis Primers"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.3","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp-2012-304636"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.4","doi-asserted-by":"publisher","DOI":"10.1097\/WCO.0b013e3283632d90"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.5","doi-asserted-by":"publisher","DOI":"10.1213\/ANE.0b013e3181c88fcd"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.6","doi-asserted-by":"crossref","first-page":"569","DOI":"10.1213\/ANE.0b013e3182917f11","article-title":"Gastric tubes and airway management in patients at risk of aspiration: history, current concepts, and proposal of an algorithm","volume":"118","author":"Salem","year":"2014","journal-title":"Anesth Analg"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.7","doi-asserted-by":"publisher","DOI":"10.1093\/bja\/aeu151"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.8","doi-asserted-by":"crossref","first-page":"262","DOI":"10.4097\/kjae.2013.64.3.262","article-title":"Anesthetic management of a patient with Huntington\u2019s chorea -A case report-","volume":"64","author":"Kang","year":"2013","journal-title":"Korean J Anesthesiol"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.9","first-page":"47","article-title":"Anaesthesia and huntington\u2019s chorea","volume":"50","author":"Yadava","year":"2006","journal-title":"Indian Journal of Anaesthesia"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.10","doi-asserted-by":"publisher","DOI":"10.1213\/ANE.0b013e3181d5ae47"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.11","first-page":"150","article-title":"Huntinton\u2019s disease: review and anaesthetic case management","volume":"35","author":"Cangemi","year":"1999","journal-title":"Anaesthetic Progress"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.12","doi-asserted-by":"publisher","DOI":"10.1590\/S0034-70942009000100013"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.13","unstructured":"Moi D . Residual neuromuscular blockade\/anaesthesia tutorial of the week 290, 2013. http:\/\/www.aagbi.org\/sites\/default\/files\/290%20Residual%20Neuromuscular%20Blockade.pdf (accessed 8 Jan 2017)."},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.14","doi-asserted-by":"publisher","DOI":"10.1093\/bja\/aev371"},{"key":"2025082804371848000_2017.oct16_1.bcr-2017-221354.15","doi-asserted-by":"publisher","DOI":"10.1111\/pan.12213"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2017-221354","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T11:37:30Z","timestamp":1756381050000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2017-221354"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,10,19]]},"references-count":15,"alternative-id":["10.1136\/bcr-2017-221354"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2017-221354","relation":{},"ISSN":["1757-790X"],"issn-type":[{"value":"1757-790X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,10,19]]}}}