{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,27]],"date-time":"2025-08-27T07:40:06Z","timestamp":1756280406047,"version":"3.44.0"},"reference-count":10,"publisher":"BMJ","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Reports"],"accepted":{"date-parts":[[2018,1,23]]},"abstract":"<jats:p>Disabling pansclerotic morphoea (DPM) of childhood is a severe and often fatal variant of deep morphoea. It usually starts in childhood and rarely seen in adults. The course of the disease is progressive with lifelong morbidity in the form of joint contractures and immobility. The causes of mortality include complications such as sepsis, gangrene and cardiopulmonary involvement. Herein, we discuss the case of a 15-year-old girl with limb deformity and finger contractures, that is, bone involvement. The diagnosis of DPM of childhood was fortuitously made after the correction of limb deformity, when the patient was seen in the dermatology department for evaluation of skin discolouration on the thighs.<\/jats:p>","DOI":"10.1136\/bcr-2017-222132","type":"journal-article","created":{"date-parts":[[2018,2,17]],"date-time":"2018-02-17T06:40:12Z","timestamp":1518849612000},"page":"bcr-2017-222132","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":3,"title":["Disabling pansclerotic morphoea of childhood"],"prefix":"10.1136","volume":"2018","author":[{"given":"Indirakshi","family":"Jamalpur","sequence":"first","affiliation":[{"name":"Department of Dermatology, Kurnool Medical College, Kurnool, Andhra Pradesh, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Harikrishna Reddy","family":"Mogili","sequence":"additional","affiliation":[{"name":"Department of Medicine, Sri Venkateswara Institute of Medical Sciences, Tirupati, Andhra Pradesh, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5801-3574","authenticated-orcid":false,"given":"Abhilash","family":"Koratala","sequence":"additional","affiliation":[{"name":"Department of Nephrology, University of Florida College of Medicine, Gainesville, Florida, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2018,2,17]]},"reference":[{"key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.1","doi-asserted-by":"crossref","first-page":"159","DOI":"10.4103\/0019-5154.108079","article-title":"Disabling pansclerotic morphea of childhood with extracutaneous manifestations","volume":"58","author":"Kura","year":"2013","journal-title":"Indian J Dermatol"},{"doi-asserted-by":"publisher","key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.2","DOI":"10.7326\/0003-4819-104-6-849"},{"key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.3","first-page":"348","article-title":"Disabling pansclerotic morphea of childhood\u2013unusual case and management challenges","volume":"1","author":"Forsea","year":"2008","journal-title":"J Med Life"},{"key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.4","doi-asserted-by":"crossref","first-page":"150","DOI":"10.1016\/j.ad.2014.06.012","article-title":"Pediatric generalized morphea that developed at a BCG vaccination site","volume":"106","author":"Matsumoto","year":"2015","journal-title":"Actas Dermosifiliogr"},{"doi-asserted-by":"publisher","key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.5","DOI":"10.1016\/j.jaad.2004.10.881"},{"doi-asserted-by":"publisher","key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.6","DOI":"10.1002\/art.21264"},{"doi-asserted-by":"publisher","key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.7","DOI":"10.1093\/rheumatology\/kel293"},{"key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.8","first-page":"2538","article-title":"Efficacy of bosentan in treatment of unresponsive cutaneous ulceration in disabling pansclerotic morphea in children","volume":"33","author":"Roldan","year":"2006","journal-title":"J Rheumatol"},{"doi-asserted-by":"publisher","key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.9","DOI":"10.1046\/j.1525-1470.2002.00235.x"},{"doi-asserted-by":"publisher","key":"2025082700023547000_2018.feb16_2.bcr-2017-222132.10","DOI":"10.1016\/j.jaad.2012.01.011"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2017-222132","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,27]],"date-time":"2025-08-27T07:02:45Z","timestamp":1756278165000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2017-222132"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,2,17]]},"references-count":10,"alternative-id":["10.1136\/bcr-2017-222132"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2017-222132","relation":{},"ISSN":["1757-790X"],"issn-type":[{"type":"electronic","value":"1757-790X"}],"subject":[],"published":{"date-parts":[[2018,2,17]]}}}