{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,21]],"date-time":"2026-03-21T00:01:29Z","timestamp":1774051289602,"version":"3.50.1"},"reference-count":34,"publisher":"BMJ","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Reports"],"accepted":{"date-parts":[[2018,3,16]]},"abstract":"<jats:p>Lymphangiomatosis is a rare developmental disorder characterised by diffuse proliferation of anastomosing lymphatic channels (lymphangiomas). It is believed to result from anomalous lymphatic development and usually presents in childhood. It typically occurs as a part of systemic lymphangiomatosis and isolated organ involvement is rare. Only nine cases of isolated cystic lymphangiomatosis of spleen have been reported between 1990 and 2010. Tuberculosis is a significant health problem in India and varied forms of this disease are seen in clinical practice. Isolated splenic tuberculosis, though a rare entity, has been described in the Indian population. We present a case of isolated splenic lymphangiomatosis in a 42-year-old woman that was initially misdiagnosed as splenic tuberculosis and was treated accordingly. Unresponsive to medical treatment, the patient underwent splenectomy and on histopathological examination, cystic lymphangiomatosis was diagnosed. The patient\u2019s symptoms resolved after surgery and she is doing well at a follow-up of 3\u2009months.<\/jats:p>","DOI":"10.1136\/bcr-2017-223856","type":"journal-article","created":{"date-parts":[[2018,4,5]],"date-time":"2018-04-05T11:25:20Z","timestamp":1522927520000},"page":"bcr-2017-223856","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Isolated cystic lymphangiomatosis of spleen in an adult: a diagnostic conundrum"],"prefix":"10.1136","volume":"2018","author":[{"given":"Pavan","family":"Kumar","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6556-8228","authenticated-orcid":false,"given":"Saket","family":"Kumar","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nuzhat","family":"Husain","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Abhijit","family":"Chandra","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2018,4,5]]},"reference":[{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.1","doi-asserted-by":"crossref","first-page":"370","DOI":"10.1053\/j.sult.2006.06.003","article-title":"Solitary splenic lesions","volume":"27","author":"Warshauer","year":"2006","journal-title":"Semin Ultrasound CT MR"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1742-1241.2004.00009.x"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.3","doi-asserted-by":"crossref","first-page":"147","DOI":"10.5858\/133.1.147","article-title":"Hamartoma of the spleen","volume":"133","author":"Lee","year":"2009","journal-title":"Arch Pathol Lab Med"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.4","doi-asserted-by":"crossref","first-page":"85","DOI":"10.59566\/IJBS.2009.5085","article-title":"Primary tumors of the spleen","volume":"5","author":"Fotiadis","year":"2009","journal-title":"Int J Biomed Sci"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.5","doi-asserted-by":"publisher","DOI":"10.1016\/S1072-7515(01)01178-4"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.6","doi-asserted-by":"publisher","DOI":"10.3748\/wjg.15.5620"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.7","doi-asserted-by":"publisher","DOI":"10.1177\/028418519003100611"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.8","doi-asserted-by":"publisher","DOI":"10.1155\/1994\/63638"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.9","doi-asserted-by":"publisher","DOI":"10.1016\/0022-3468(91)90607-U"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.10","doi-asserted-by":"publisher","DOI":"10.1148\/radiology.175.2.2183287"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.11","doi-asserted-by":"publisher","DOI":"10.1259\/bjr\/93530580"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.12","doi-asserted-by":"publisher","DOI":"10.1001\/jama.1976.03270210041022"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.13","doi-asserted-by":"publisher","DOI":"10.1016\/S0730-725X(02)00624-0"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.14","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9343(64)90138-X"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.15","doi-asserted-by":"crossref","first-page":"173","DOI":"10.1148\/radiology.202.1.8988208","article-title":"Splenic lymphangiomatosis in children","volume":"202","author":"Wadsworth","year":"1997","journal-title":"Radiology"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.16","doi-asserted-by":"publisher","DOI":"10.3748\/wjg.v16.i9.1155"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.17","first-page":"599","article-title":"The clinical spectrum of lymphangiomas and lymphangiomatosis of the spleen","volume":"58","author":"Morgenstern","year":"1992","journal-title":"Am Surg"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.18","doi-asserted-by":"publisher","DOI":"10.2214\/ajr.147.3.537"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.19","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3468(89)80711-0"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.20","first-page":"555","article-title":"[Cystic splenic disease of surgical interest]","volume":"18","author":"Gidaro","year":"1997","journal-title":"G Chir"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.21","doi-asserted-by":"publisher","DOI":"10.1148\/rg.244045006"},{"key":"2025042703192572000_2018.apr05_1.bcr-2017-223856.22","first-page":"159","article-title":"[Intraabdominal cystic lymphangioma in childhood. 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