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There are only four patients reported to be affected by cerebellar atrophy associated with PSS. Administration of high doses of methylprednisolone and cyclophosphamide leads to substantial improvement in the cerebellar symptoms of this case. In addition, after 2\u2009months of follow-up, the patient\u2019s ataxia recovered significantly. It could be concluded that in addition to neurological degenerative disorders, in some cases cerebellar atrophy could also be associated with autoimmune conditions such as PSS.<\/jats:p>","DOI":"10.1136\/bcr-2017-223952","type":"journal-article","created":{"date-parts":[[2018,6,7]],"date-time":"2018-06-07T06:00:04Z","timestamp":1528351204000},"page":"bcr-2017-223952","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":8,"title":["Cerebellar degeneration in primary Sj\u04e7gren syndrome"],"prefix":"10.1136","volume":"2018","author":[{"given":"Mohammad","family":"Heidary","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3860-0787","authenticated-orcid":false,"given":"Samira","family":"Alesaeidi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Khashayar","family":"Afshari","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2018,6,6]]},"reference":[{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.1","doi-asserted-by":"publisher","DOI":"10.1097\/01.md.0000141099.53742.16"},{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.2","doi-asserted-by":"publisher","DOI":"10.2165\/00003495-200464020-00001"},{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.3","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.57.3.411"},{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.4","first-page":"59","article-title":"Neurologic disease in Sj\u00f6gren\u2019s syndrome","volume":"71","author":"Alexander","year":"1998","journal-title":"Handbook of clinical neurology"},{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.5","doi-asserted-by":"publisher","DOI":"10.1001\/archinte.164.12.1275"},{"issue":"s1","key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.6","doi-asserted-by":"crossref","first-page":"39","DOI":"10.1111\/j.1834-7819.2010.01197.x","article-title":"Sj\u00f6gren\u2019s syndrome: a review of aetiology, pathogenesis, diagnosis and management","volume":"55 Suppl 1","author":"Bayetto","year":"2010","journal-title":"Aust Dent J"},{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.7","doi-asserted-by":"publisher","DOI":"10.1016\/j.autrev.2009.11.004"},{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.8","doi-asserted-by":"publisher","DOI":"10.1136\/annrheumdis-2014-205375"},{"key":"2025042703494186000_2018.jun06_1.bcr-2017-223952.9","doi-asserted-by":"crossref","unstructured":"Skopouli FN , Dafni U , Ioannidis JPA , et al . 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