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Genetic testing of the specimen provided evidence of microsatellite instability and faulty DNA repair supporting aetiology of Lynch syndrome. This case is unique in that SBA, if present in patients with Lynch syndrome, is usually a presenting symptom and has not been widely described in literature as an occurrence so many years after. As a result, this case highlights the importance of a low threshold for a thorough evaluation in patients with Lynch syndrome who present with signs of small bowel obstruction.<\/jats:p>","DOI":"10.1136\/bcr-2018-225003","type":"journal-article","created":{"date-parts":[[2018,6,4]],"date-time":"2018-06-04T13:24:39Z","timestamp":1528118679000},"page":"bcr-2018-225003","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":3,"title":["Patient with Lynch syndrome with subsequent development of small bowel adenocarcinoma"],"prefix":"10.1136","volume":"2018","author":[{"given":"Abdul Hussain","family":"Azizi","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Zaina S","family":"Inam","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Timothy J","family":"Farrell","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2018,6,4]]},"reference":[{"key":"2025042703470480000_2018.jun01_1.bcr-2018-225003.1","doi-asserted-by":"publisher","DOI":"10.1016\/j.dld.2013.04.013"},{"key":"2025042703470480000_2018.jun01_1.bcr-2018-225003.2","doi-asserted-by":"publisher","DOI":"10.3322\/caac.21387"},{"key":"2025042703470480000_2018.jun01_1.bcr-2018-225003.3","first-page":"1364","article-title":"Management of small bowel adenocarcinoma","volume":"16","author":"Kummar","year":"2002","journal-title":"Oncology"},{"key":"2025042703470480000_2018.jun01_1.bcr-2018-225003.4","doi-asserted-by":"crossref","first-page":"1602","DOI":"10.3892\/ol.2016.4753","article-title":"Small bowel adenocarcinoma in Lynch syndrome: A case report","volume":"12","author":"Sun","year":"2016","journal-title":"Oncol Lett"},{"key":"2025042703470480000_2018.jun01_1.bcr-2018-225003.5","doi-asserted-by":"crossref","first-page":"509","DOI":"10.4251\/wjgo.v8.i6.509","article-title":"Genetic risks and familial associations of small bowel carcinoma","volume":"8","author":"Shenoy","year":"2016","journal-title":"World J Gastrointest Oncol"},{"key":"2025042703470480000_2018.jun01_1.bcr-2018-225003.6","doi-asserted-by":"crossref","first-page":"217","DOI":"10.4166\/kjg.2011.58.4.217","article-title":"Small bowel carcinoma in young patient detected by double-balloon enteroscopy","volume":"58","author":"Choi","year":"2011","journal-title":"Korean J Gastroenterol"},{"key":"2025042703470480000_2018.jun01_1.bcr-2018-225003.7","unstructured":"American Joint Committee on Cancer. 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