{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,17]],"date-time":"2026-07-17T20:07:23Z","timestamp":1784318843462,"version":"3.55.0"},"reference-count":12,"publisher":"BMJ","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Reports"],"accepted":{"date-parts":[[2018,8,4]]},"abstract":"<jats:p>A 61-year-old Caucasian man presented with a fever of unknown origin, a transient erythematous rash on his right upper extremity and chest pressure after being treated for erythema migrans (Lyme disease). Echocardiogram demonstrated a large pericardial effusion with tamponade. He underwent pericardiostomy with tube placement. Workup for infectious and malignant etiologies was negative. Histology of the pericardium showed acute on chronic fibrinous haemorrhagic pericarditis. The patient met criteria for adult-onset Still\u2019s disease. Symptoms resolved following treatment with methylprednisolone and anakinra. We believe this is the first case of adult-onset Still\u2019s disease precipitated by acute Lyme disease.<\/jats:p>","DOI":"10.1136\/bcr-2018-225517","type":"journal-article","created":{"date-parts":[[2018,8,16]],"date-time":"2018-08-16T09:55:31Z","timestamp":1534413331000},"page":"bcr-2018-225517","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":9,"title":["Adult-onset Still\u2019s disease with haemorrhagic pericarditis and tamponade preceded by acute Lyme disease"],"prefix":"10.1136","volume":"2018","author":[{"given":"Anthony J","family":"Ocon","sequence":"first","affiliation":[{"name":"Internal Medicine, Albany Medical College, Albany, New York, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alysia V","family":"Kwiatkowski","sequence":"additional","affiliation":[{"name":"Internal Medicine, Division of Rheumatology, Rush University, Chicago, Illinois, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ruben","family":"Peredo-Wende","sequence":"additional","affiliation":[{"name":"Internal Medicine, Division of Rheumatology, Albany Medical College, Albany, New York, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Richard","family":"Blinkhorn","sequence":"additional","affiliation":[{"name":"Internal Medicine, Division of Infectious Diseases, Albany Medical College, Albany, New York, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2018,8,16]]},"reference":[{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.1","doi-asserted-by":"crossref","first-page":"277","DOI":"10.14503\/THIJ-14-4101","article-title":"Adult-onset Still\u2019s disease and cardiac tamponade: a rare association","volume":"42","author":"Carrilho-Ferreira","year":"2015","journal-title":"Tex Heart Inst J"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.2","first-page":"424","article-title":"Preliminary criteria for classification of adult Still\u2019s disease","volume":"19","author":"Yamaguchi","year":"1992","journal-title":"J Rheumatol"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.3","doi-asserted-by":"publisher","DOI":"10.1016\/j.revmed.2006.03.027"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.4","doi-asserted-by":"publisher","DOI":"10.1016\/j.autrev.2014.01.058"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.5","first-page":"305","article-title":"Lyme arthritis presenting as adult onset Still\u2019s disease","volume":"7","author":"Cimmino","year":"1989","journal-title":"Clin Exp Rheumatol"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.6","doi-asserted-by":"crossref","first-page":"R39","DOI":"10.1186\/ar4193","article-title":"Involvement of TLR7 MyD88-dependent signaling pathway in the pathogenesis of adult-onset Still\u2019s disease","volume":"15","author":"Chen","year":"2013","journal-title":"Arthritis Res Ther"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.7","first-page":"233","article-title":"Innate immunity networks during infection with Borrelia burgdorferi","volume":"42","author":"Oosting","year":"2016","journal-title":"Crit Rev Microbiol"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.8","doi-asserted-by":"publisher","DOI":"10.1002\/eji.201040385"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.9","doi-asserted-by":"crossref","first-page":"90","DOI":"10.1016\/j.autrev.2014.10.005","article-title":"Autoimmunity and autoinflammation as the yin and yang of idiopathic recurrent acute pericarditis","volume":"14","author":"Cantarini","year":"2015","journal-title":"Autoimmun Rev"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.10","unstructured":"KINERET\u00ae (anakinra) injection prescribing information. Stockholm, Sweden: Swedish Orphan Biovitrum AB, 2015."},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.11","doi-asserted-by":"crossref","first-page":"1277","DOI":"10.1016\/j.amjcard.2015.07.047","article-title":"Effectiveness and safety of anakinra for management of refractory pericarditis","volume":"116","author":"Jain","year":"2015","journal-title":"Am J Cardiol"},{"key":"2025082803101290000_2018.aug16_1.bcr-2018-225517.12","doi-asserted-by":"crossref","first-page":"429","DOI":"10.1007\/s00281-015-0501-9","article-title":"Regulating against the dysregulation: new treatment options in autoinflammation","volume":"37","author":"Kallinich","year":"2015","journal-title":"Semin Immunopathol"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2018-225517","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T10:10:18Z","timestamp":1756375818000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2018-225517"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2018,8,16]]},"references-count":12,"alternative-id":["10.1136\/bcr-2018-225517"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2018-225517","relation":{},"ISSN":["1757-790X"],"issn-type":[{"value":"1757-790X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2018,8,16]]}}}