{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,1]],"date-time":"2026-05-01T12:14:30Z","timestamp":1777637670718,"version":"3.51.4"},"reference-count":12,"publisher":"BMJ","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Reports"],"accepted":{"date-parts":[[2018,9,12]]},"abstract":"<jats:p>Leiomyosarcoma (LMS) of primary vascular origin is a rare entity with only potentially curative option being complete surgical resection; despite which the prognosis remains dismal. Tumour recurrence is very common, and the benefits of adjuvant therapy are undefined. A 39-year-old woman presented with 6 months\u2019 history of abdominal pain, abdominal distension and pedal oedema. On evaluation, she was diagnosed to have chronic Budd-Chiari syndrome (BCS) secondary to a tumour arising from the inferior vena cava (IVC) on evaluation. Her liver decompensation included jaundice, gastrointestinal bleed and ascites. Following a detailed multidisciplinary team discussion, she underwent complete excision of the tumour along with a segment of the IVC with living donor liver transplantation. She remains disease-free 24 months following surgery. This is the first reported case of liver transplantation for IVC LMS causing chronic BCS.<\/jats:p>","DOI":"10.1136\/bcr-2018-225827","type":"journal-article","created":{"date-parts":[[2018,9,29]],"date-time":"2018-09-29T02:51:44Z","timestamp":1538189504000},"page":"bcr-2018-225827","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Liver transplantation for inferior vena cava leiomyosarcoma: from a Maslow\u2019s hammer to the Occam\u2019s razor"],"prefix":"10.1136","volume":"2018","author":[{"given":"Vasanthakumar","family":"Gunasekaran","sequence":"first","affiliation":[{"name":"Institute of Liver Disease & Transplantation, Gleneagles Global Health City, Chennai, Tamil Nadu, India"},{"name":"Institute of Liver Disease & Transplantation, Dr.Rela Institute & Medical Centre, Bharat Institute of Higher Education & Research, Chennai, Tamil Nadu, 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