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Herein, we report the presentation of a newly diagnosed 13-month-old child with immunodeficiency 31B after presenting with disseminated measles and varicella infection after Measles, Mumps, Rubella and Varicella vaccination.<\/jats:p>","DOI":"10.1136\/bcr-2019-233063","type":"journal-article","created":{"date-parts":[[2020,1,22]],"date-time":"2020-01-22T05:16:18Z","timestamp":1579670178000},"page":"e233063","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Diagnosing inborn error of immunity following the presentation of a complicated acquired infection after MMRV vaccine administration"],"prefix":"10.1136","volume":"13","author":[{"given":"Lama","family":"AlZoebie","sequence":"first","affiliation":[{"name":"Pediatrics, Sheikh Khalifa Medical City, Abu Dhabi, United Arab Emirates"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hend","family":"Al Sereidi","sequence":"additional","affiliation":[{"name":"Paediatric Critical Care Medicine, Shaikh Khalifa Medical City, Abu Dhabi, United Arab Emirates"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shaima","family":"Al Maeeni","sequence":"additional","affiliation":[{"name":"Paediatric Critical Care Medicine, Shaikh Khalifa Medical City, Abu Dhabi, United Arab Emirates"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Musaab","family":"Ramsi","sequence":"additional","affiliation":[{"name":"Paediatric Critical Care Medicine, Shaikh Khalifa Medical City, Abu Dhabi, United Arab Emirates"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2020,1,21]]},"reference":[{"key":"2025082622394038000_13.1.e233063.1","doi-asserted-by":"crossref","first-page":"527","DOI":"10.1007\/s10875-019-00653-0","article-title":"Correction to: life-threatening infections due to live-attenuated vaccines: early manifestations of inborn errors of immunity","volume":"39","author":"P\u00f6yh\u00f6nen","year":"2019","journal-title":"J Clin Immunol"},{"key":"2025082622394038000_13.1.e233063.2","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2010-04-280586"},{"key":"2025082622394038000_13.1.e233063.3","unstructured":"U.S. National Library of Medicine. 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