{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,28]],"date-time":"2026-03-28T13:06:57Z","timestamp":1774703217719,"version":"3.50.1"},"reference-count":31,"publisher":"BMJ","issue":"2","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2020,2,6]]},"published-print":{"date-parts":[[2020,2]]},"abstract":"<jats:p>A 7-year-old child who suffered from symptomatic focal epilepsy as a sequel to perinatal hypoxia used to have frequent seizures. This time she developed prolonged status epilepticus lasting for over 5\u2009hours. She received a treatment in the form of intravenous midazolam and reinitiation of sodium valproate and clobazam that were discontinued previously. Seizures were controlled over a couple of hours, but she remained unresponsive. Later, she developed acute onset dystonia (day 3 post-status epilepticus) and also myoclonic jerks. She presented to us after 3 weeks of onset of these complaints and we considered hypoxic encephalopathy resulting from prolonged status epilepticus or acute encephalitis or non-convulsive status epilepticus. However, acute onset dystonia and periodicity of myoclonic jerks were pointers against it, and on evaluation, she was diagnosed with atypical fulminant subacute sclerosing panencephalitis (SSPE). Knowing the atypical presentations of SSPE is important in planning management and prognostication.<\/jats:p>","DOI":"10.1136\/bcr-2019-233397","type":"journal-article","created":{"date-parts":[[2020,2,28]],"date-time":"2020-02-28T14:25:20Z","timestamp":1582899920000},"page":"e233397","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":4,"title":["Clinical conundrum: status epilepticus culminating into acute dystonia myoclonus"],"prefix":"10.1136","volume":"13","author":[{"given":"Madhuri Laxman","family":"Khilari","sequence":"first","affiliation":[{"name":"Neurology, Apollo Hospitals, Hyderabad, Telangana, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Praveen Kumar","family":"Sharma","sequence":"additional","affiliation":[{"name":"Neurology, King George Medical University, Lucknow, Uttar Pradesh, India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2020,2,28]]},"reference":[{"key":"2025082703343014000_13.2.e233397.1","doi-asserted-by":"crossref","first-page":"732","DOI":"10.4103\/0972-2327.120437","article-title":"A rare presentation of subacute sclerosing panencephalitis with acute fulminant course and atypical radiological features","volume":"16","author":"Jain","year":"2013","journal-title":"Ann Indian Acad Neurol"},{"key":"2025082703343014000_13.2.e233397.2","first-page":"354","volume-title":"Fulminant subacute sclerosing panencephalitis presenting with acute ataxia and hemiparesis in a 15-year-old boy","volume":"10","author":"Kandadai","year":"2014"},{"key":"2025082703343014000_13.2.e233397.3","doi-asserted-by":"publisher","DOI":"10.1001\/archneurol.2011.240"},{"key":"2025082703343014000_13.2.e233397.4","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1973.00490190028002"},{"key":"2025082703343014000_13.2.e233397.5","doi-asserted-by":"crossref","first-page":"22ii","DOI":"10.1136\/jnnp.70.suppl_2.ii22","article-title":"The management of status epilepticus","volume":"70","author":"Shorvon","year":"2001","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"2025082703343014000_13.2.e233397.6","doi-asserted-by":"publisher","DOI":"10.1111\/j.1528-1157.2000.tb00206.x"},{"key":"2025082703343014000_13.2.e233397.7","doi-asserted-by":"publisher","DOI":"10.1177\/0885066615571533"},{"key":"2025082703343014000_13.2.e233397.8","doi-asserted-by":"publisher","DOI":"10.1016\/j.ncl.2005.11.001"},{"key":"2025082703343014000_13.2.e233397.9","doi-asserted-by":"crossref","first-page":"292","DOI":"10.4103\/0972-2327.138503","article-title":"Movement disorders of probable infectious origin","volume":"17","author":"Jhunjhunwala","year":"2014","journal-title":"Ann Indian Acad Neurol"},{"key":"2025082703343014000_13.2.e233397.10","doi-asserted-by":"crossref","first-page":"250","DOI":"10.3389\/fped.2017.00250","article-title":"Pediatric Anti-N-Methyl-d-Aspartate Receptor Encephalitis: A Review with Pooled Analysis and Critical Care Emphasis","volume":"5","author":"Remy","year":"2017","journal-title":"Front Pediatr"},{"key":"2025082703343014000_13.2.e233397.11","doi-asserted-by":"crossref","first-page":"179","DOI":"10.1016\/S0733-8619(18)31062-4","article-title":"Subacute sclerosing panencephalitis. current status","volume":"3","author":"Dyken","year":"1985","journal-title":"Neurol Clin"},{"key":"2025082703343014000_13.2.e233397.12","doi-asserted-by":"publisher","DOI":"10.2165\/00003495-198632050-00001"},{"key":"2025082703343014000_13.2.e233397.13","doi-asserted-by":"crossref","first-page":"1034","DOI":"10.1016\/S0140-6736(82)92097-9","article-title":"Inosiplex therapy in subacute sclerosing panencephalitis. 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