{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,24]],"date-time":"2026-09-24T11:20:27Z","timestamp":1790248827248,"version":"4.1.0"},"reference-count":6,"publisher":"BMJ","issue":"9","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2020,8,5]]},"published-print":{"date-parts":[[2020,9]]},"abstract":"<jats:p>A 35-year-old man with Ehlers-Danlos syndrome type IV (EDS IV) underwent surgical repair of an enteroatmospheric fistula. Despite the substantially increased operative risk, repair was undertaken in view of his poor quality of life and severe nutritional deficits. Dense adhesions and extremely fragile bowel and vasculature characteristic of EDS IV were encountered intraoperatively. Multiple traction enterotomies and faecal matter leaking from suture holes necessitated leaving the abdomen open for a prolonged period. An Abdominal Reapproximation Anchor device was applied to prevent lateral retraction of the abdominal wall during this time. At relook on day 6, no leak was found, and the abdomen was closed. Two years postoperatively, the patient has an intact abdominal wall, with a vastly improved quality of life. This case illustrates the challenges of operating on patients with EDS IV, and presents a novel technique in managing fistulas in these patients.<\/jats:p>","DOI":"10.1136\/bcr-2020-234670","type":"journal-article","created":{"date-parts":[[2020,9,23]],"date-time":"2020-09-23T17:11:29Z","timestamp":1600881089000},"page":"e234670","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":3,"title":["Enteroatmospheric fistula repair in Ehlers-Danlos syndrome type IV: a novel management technique using ABRA device"],"prefix":"10.1136","volume":"13","author":[{"given":"Omar","family":"Zubair","sequence":"first","affiliation":[{"name":"Surgery, Princess Alexandra Hospital, Woolloongabba, Queensland, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kellee","family":"Slater","sequence":"additional","affiliation":[{"name":"Surgery, Greenslopes Private Hospital, Brisbane, Queensland, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2020,9,23]]},"reference":[{"key":"2025082802180604000_13.9.e234670.1","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1007\/s10151-018-1783-4","article-title":"Bowel perforation in type IV vascular Ehlers\u2013Danlos syndrome. A systematic review","volume":"22","author":"El Masri","year":"2018","journal-title":"Tech Coloproctol"},{"key":"2025082802180604000_13.9.e234670.2","doi-asserted-by":"crossref","first-page":"161","DOI":"10.1159\/000449106","article-title":"Increased need for gastrointestinal surgery and increased risk of surgery-related complications in patients with Ehlers-Danlos syndrome: a systematic review","volume":"34","author":"Kulas S\u00f8borg","year":"2017","journal-title":"Dig Surg"},{"key":"2025082802180604000_13.9.e234670.3","doi-asserted-by":"crossref","first-page":"349","DOI":"10.1159\/000343738","article-title":"Gastrointestinal surgery and related complications in patients with Ehlers-Danlos syndrome: a systematic review","volume":"29","author":"Burcharth","year":"2012","journal-title":"Dig Surg"},{"key":"2025082802180604000_13.9.e234670.4","doi-asserted-by":"publisher","DOI":"10.1007\/s00268-011-1210-8"},{"key":"2025082802180604000_13.9.e234670.5","doi-asserted-by":"publisher","DOI":"10.1002\/(SICI)1096-8628(19980428)77:1<31::AID-AJMG8>3.0.CO;2-O"},{"key":"2025082802180604000_13.9.e234670.6","first-page":"209","article-title":"Management of open abdominal wounds with a dynamic fascial closure system","volume":"51","author":"Reimer","year":"2008","journal-title":"Can J Surg"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2020-234670","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T09:18:13Z","timestamp":1756372693000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2020-234670"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,9]]},"references-count":6,"journal-issue":{"issue":"9","published-online":{"date-parts":[[2020,9,23]]},"published-print":{"date-parts":[[2020,9]]}},"alternative-id":["10.1136\/bcr-2020-234670"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2020-234670","relation":{},"ISSN":["1757-790X"],"issn-type":[{"value":"1757-790X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,9]]}}}