{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,8,29]],"date-time":"2025-08-29T00:03:19Z","timestamp":1756425799558,"version":"3.44.0"},"reference-count":22,"publisher":"BMJ","issue":"3","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2021,3,2]]},"published-print":{"date-parts":[[2021,3]]},"abstract":"<jats:p>Klippel-Feil syndrome is an entity presenting with short neck, low hairline and reduced range of motion of cervical spine. Neurenteric cyst is a congenital abnormality, in which mucus-secreting epithelium of the gastrointestinal tract is seen in the spinal axis. The association of a neurenteric cyst with Klippel-Feil syndrome has been reported very rarely. We report the case of a young man, affected by Klippel-Feil syndrome, who presented with bilateral paraplegia. Imaging of the spine revealed features suggestive of cervico-dorsal neurenteric cyst. Subsequently, surgical resection of the cysts was done, which resulted in resolution of the symptoms.<\/jats:p>","DOI":"10.1136\/bcr-2020-235327","type":"journal-article","created":{"date-parts":[[2021,3,18]],"date-time":"2021-03-18T13:10:25Z","timestamp":1616073025000},"page":"e235327","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Rare cause of paraparesis in a young man: cervico-dorsal neurenteric cysts associated with Klippel-Feil syndrome"],"prefix":"10.1136","volume":"14","author":[{"given":"Raghav","family":"Seth","sequence":"first","affiliation":[{"name":"Radiodiagnosis, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-5034-3488","authenticated-orcid":false,"given":"Anindita","family":"Sinha","sequence":"additional","affiliation":[{"name":"Radiodiagnosis, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Navneet","family":"Singla","sequence":"additional","affiliation":[{"name":"Neurosurgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Debajyoti","family":"Chatterjee","sequence":"additional","affiliation":[{"name":"Histopathology, Post Graduate Institute of Medical Education and Research, Chandigarh, India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2021,3,18]]},"reference":[{"key":"2025082801422491000_14.3.e235327.1","first-page":"50","article-title":"KLIPPEL-FEIL's syndrome","volume":"11","author":"Gjorup","year":"1964","journal-title":"Dan Med Bull"},{"key":"2025082801422491000_14.3.e235327.2","doi-asserted-by":"crossref","first-page":"179","DOI":"10.1097\/01202412-199807000-00001","article-title":"Assessment and neurologic involvement of patients with cervical spine congenital Synostosis as in Klippel-Feil syndrome: study of 19 cases","volume":"7","author":"Rouvreau","year":"1998","journal-title":"J Pediatr Orthop B"},{"key":"2025082801422491000_14.3.e235327.3","doi-asserted-by":"crossref","first-page":"343","DOI":"10.1097\/01241398-198905000-00017","article-title":"Klippel-Feil syndrome with neck pain","volume":"9","author":"Herring","year":"1989","journal-title":"J Pediatr Orthop"},{"key":"2025082801422491000_14.3.e235327.4","first-page":"e3379","article-title":"Comprehensive review of spinal neurenteric cysts with a focus on histopathological findings","volume":"10","author":"Baek","year":"2018","journal-title":"Cureus"},{"key":"2025082801422491000_14.3.e235327.5","doi-asserted-by":"publisher","DOI":"10.1007\/BF01401186"},{"key":"2025082801422491000_14.3.e235327.6","first-page":"373","article-title":"Congenital fusion of the cervical vertebrae","volume":"118","author":"Gray","year":"1964","journal-title":"Surg Gynecol Obstet"},{"key":"2025082801422491000_14.3.e235327.7","doi-asserted-by":"publisher","DOI":"10.1097\/00005792-196711000-00003"},{"key":"2025082801422491000_14.3.e235327.8","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320260424"},{"key":"2025082801422491000_14.3.e235327.9","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.37263"},{"key":"2025082801422491000_14.3.e235327.10","unstructured":"Menger RP , Notarianni C . 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