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However, the disease pathology can involve the central nervous system. This case report presents a case of GPA with facial nerve palsy as the first manifestation of the disease, which has been rarely reported in the medical literature.<\/jats:p>","DOI":"10.1136\/bcr-2020-236469","type":"journal-article","created":{"date-parts":[[2021,1,12]],"date-time":"2021-01-12T03:45:24Z","timestamp":1610423124000},"page":"e236469","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":7,"title":["Granulomatosis with polyangiitis presenting with unilateral facial nerve palsy and nasal septum perforation"],"prefix":"10.1136","volume":"14","author":[{"given":"Bandar","family":"Zaeri","sequence":"first","affiliation":[{"name":"Internal Medice Department, King Saud Medical City, Riyadh, Saudi Arabia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Soha","family":"Khan","sequence":"additional","affiliation":[{"name":"Internal Medice Department, King Saud Medical City, Riyadh, Saudi 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