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Characteristic skin lesions such as caf\u00e9-au-lait macules and neurofibromas contributed to the diagnosis of NF1 and pheochromocytoma. No recurrence of electrolyte depletion was found after the adrenalectomy. Primary care physicians must distinguish the characteristic skin lesions of NF1, such as caf\u00e9-au-lait macules and neurofibromas and recognise the risk for pheochromocytoma.<\/jats:p>","DOI":"10.1136\/bcr-2020-237231","type":"journal-article","created":{"date-parts":[[2021,1,25]],"date-time":"2021-01-25T11:26:33Z","timestamp":1611573993000},"page":"e237231","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":1,"title":["Pheochromocytoma crisis in a patient with newly diagnosed neurofibromatosis type 1"],"prefix":"10.1136","volume":"14","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-5119-4982","authenticated-orcid":false,"given":"Hisashi","family":"Murakami","sequence":"first","affiliation":[{"name":"Emergency and Critical Care Medicine, Hitachi General Hospital, Hitachi, Ibaraki, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tomohiro","family":"Sonoo","sequence":"additional","affiliation":[{"name":"Emergency and Critical Care Medicine, Hitachi General Hospital, Hitachi, Ibaraki, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hideki","family":"Hashimoto","sequence":"additional","affiliation":[{"name":"Emergency and Critical Care Medicine, Hitachi General Hospital, Hitachi, Ibaraki, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kensuke","family":"Nakamura","sequence":"additional","affiliation":[{"name":"Emergency and Critical Care Medicine, Hitachi General Hospital, Hitachi, Ibaraki, Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2021,1,25]]},"reference":[{"key":"2025082623533812000_14.1.e237231.1","doi-asserted-by":"publisher","DOI":"10.1177\/000992289603501101"},{"key":"2025082623533812000_14.1.e237231.2","doi-asserted-by":"crossref","first-page":"98","DOI":"10.1055\/s-0036-1579766","article-title":"Neurofibromatosis: a review of NF1, NF2, and schwannomatosis","volume":"5","author":"Kresak","year":"2016","journal-title":"J Pediatr Genet"},{"key":"2025082623533812000_14.1.e237231.3","doi-asserted-by":"publisher","DOI":"10.1001\/jama.1997.03550010065042"},{"key":"2025082623533812000_14.1.e237231.4","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-5347(05)68171-2"},{"key":"2025082623533812000_14.1.e237231.5","doi-asserted-by":"publisher","DOI":"10.1016\/j.pcl.2010.07.002"},{"key":"2025082623533812000_14.1.e237231.6","doi-asserted-by":"publisher","DOI":"10.1016\/S1474-4422(14)70063-8"},{"key":"2025082623533812000_14.1.e237231.7","doi-asserted-by":"publisher","DOI":"10.1016\/j.jaad.2008.12.051"},{"key":"2025082623533812000_14.1.e237231.8","first-page":"152","article-title":"Neurofibromatosis type 1 with interstitial pulmonary lesions diagnosed in adult patient. 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