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The rarity may be due to the two associated conditions being under-reported, undiagnosed, misdiagnosed or possibly the association is rare on the African continent. The clinician dealing with these two conditions should be aware of the association.<\/jats:p>","DOI":"10.1136\/bcr-2020-238380","type":"journal-article","created":{"date-parts":[[2021,5,10]],"date-time":"2021-05-10T13:55:15Z","timestamp":1620654915000},"page":"e238380","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Association between pheochromocytoma and neurofibromatosis type I: a rare entity in the African population"],"prefix":"10.1136","volume":"14","author":[{"given":"Brandon S","family":"Jackson","sequence":"first","affiliation":[{"name":"Surgery, Kalafong Provincial Tertiary Hospital, University of Pretoria, Pretoria, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Maryke","family":"De Villiers","sequence":"additional","affiliation":[{"name":"Internal Medicine, Kalafong Provincial Tertiary Hospital, University of Pretoria, Pretoria, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Daniel","family":"Montwedi","sequence":"additional","affiliation":[{"name":"Surgery, Kalafong Provincial Tertiary Hospital, University of Pretoria, Pretoria, South Africa"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2021,5,10]]},"reference":[{"key":"2025082712081723000_14.5.e238380.1","doi-asserted-by":"publisher","DOI":"10.1196\/annals.1353.013"},{"key":"2025082712081723000_14.5.e238380.2","doi-asserted-by":"publisher","DOI":"10.1093\/jnci\/djg024"},{"key":"2025082712081723000_14.5.e238380.3","doi-asserted-by":"crossref","first-page":"1459","DOI":"10.1056\/NEJMoa020152","article-title":"Germ-line mutations in nonsyndromic pheochromocytoma","volume":"346","author":"Neumann","year":"2002","journal-title":"N Engl J Med Overseas Ed"},{"key":"2025082712081723000_14.5.e238380.4","doi-asserted-by":"publisher","DOI":"10.1093\/hmg\/11.20.2347"},{"key":"2025082712081723000_14.5.e238380.5","doi-asserted-by":"publisher","DOI":"10.1002\/(SICI)1096-8628(19990326)89:1<1::AID-AJMG3>3.0.CO;2-8"},{"key":"2025082712081723000_14.5.e238380.6","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.2006.045906"},{"key":"2025082712081723000_14.5.e238380.7","doi-asserted-by":"publisher","DOI":"10.1016\/S1471-4914(01)01955-4"},{"key":"2025082712081723000_14.5.e238380.8","unstructured":"Viskochil DH . 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