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Here we report a case of a 38-year-old man who presented with chronic additive large and small joint inflammatory polyarthritis, associated with morning stiffness, anasarca associated with frothy urine and progressive episodic, relapsing and remitting, sensorimotor lower motor neuron type quadriparesis without any bladder and bowel involvement. He was diagnosed as a case of CIDP, and the aetiology was found out to be mixed connective tissue disorder, which is a rare association with CIDP. The patient responded dramatically to glucocorticoid.<\/jats:p>","DOI":"10.1136\/bcr-2020-238519","type":"journal-article","created":{"date-parts":[[2021,4,22]],"date-time":"2021-04-22T11:32:33Z","timestamp":1619091153000},"page":"e238519","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":4,"title":["Case of rare association of peripheral neuropathy with mixed connective tissue disorder"],"prefix":"10.1136","volume":"14","author":[{"given":"Prativa Priyadarshani","family":"Sethi","sequence":"first","affiliation":[{"name":"Internal Medicine, All India Institute Of Medical Science, Rishikesh, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Aditya","family":"Sudan","sequence":"additional","affiliation":[{"name":"Internal Medicine, All India Institute Of Medical Science, Rishikesh, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Suman","family":"Kumari","sequence":"additional","affiliation":[{"name":"Pathology, All India Institute of Medical Science, Rishikesh, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-3609-1162","authenticated-orcid":false,"given":"Monika","family":"Pathania","sequence":"additional","affiliation":[{"name":"Internal Medicine, All India Institute Of Medical Science, Rishikesh, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2021,4,22]]},"reference":[{"key":"2025082800074087000_14.4.e238519.1","doi-asserted-by":"publisher","DOI":"10.1016\/j.semarthrit.2005.08.008"},{"key":"2025082800074087000_14.4.e238519.2","doi-asserted-by":"crossref","first-page":"508","DOI":"10.1097\/WCO.0000000000000481","article-title":"Chronic inflammatory demyelinating polyneuropathy","volume":"30","author":"Lewis","year":"2017","journal-title":"Curr Opin Neurol"},{"key":"2025082800074087000_14.4.e238519.3","doi-asserted-by":"crossref","first-page":"485","DOI":"10.1016\/j.jbspin.2017.02.013","article-title":"Lewis-Sumner syndrome in a patient with rheumatoid arthritis: link between rheumatoid arthritis and demyelinating polyradiculoneuropathies","volume":"84","author":"Kedra","year":"2017","journal-title":"Joint Bone Spine"},{"key":"2025082800074087000_14.4.e238519.4","doi-asserted-by":"publisher","DOI":"10.1159\/000494291"},{"key":"2025082800074087000_14.4.e238519.5","doi-asserted-by":"crossref","first-page":"371","DOI":"10.1002\/mus.25203","article-title":"Electrodiagnostic reference values for upper and lower limb nerve conduction studies in adult populations","volume":"54","author":"Chen","year":"2016","journal-title":"Muscle Nerve"},{"key":"2025082800074087000_14.4.e238519.6","doi-asserted-by":"publisher","DOI":"10.1111\/j.1468-1331.2009.02930.x"},{"key":"2025082800074087000_14.4.e238519.7","first-page":"S225","article-title":"Guidelines in Electrodiagnostic medicine. consensus criteria for the diagnosis of partial conduction block","volume":"8","author":"Olney","year":"1999","journal-title":"Muscle Nerve Suppl"},{"key":"2025082800074087000_14.4.e238519.8","doi-asserted-by":"publisher","DOI":"10.1016\/j.autrev.2006.03.004"},{"key":"2025082800074087000_14.4.e238519.9","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1186\/s13075-017-1494-7","article-title":"Disease evolution in mixed connective tissue disease: results from a long-term nationwide prospective cohort study","volume":"19","author":"Reiseter","year":"2017","journal-title":"Arthritis Res Ther"},{"key":"2025082800074087000_14.4.e238519.10","doi-asserted-by":"publisher","DOI":"10.1136\/jnnp.2005.081547"},{"key":"2025082800074087000_14.4.e238519.11","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9343(72)90064-2"},{"key":"2025082800074087000_14.4.e238519.12","unstructured":"Tanaka K , Tanaka M . 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