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We report a case of EVC who presented for the first time at 60 years of age, as survival to an advanced age is exceptional in case of EVC.<\/jats:p>","DOI":"10.1136\/bcr-2020-239663","type":"journal-article","created":{"date-parts":[[2021,3,24]],"date-time":"2021-03-24T12:45:57Z","timestamp":1616589957000},"page":"e239663","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":1,"title":["Late survival in Ellis-van Creveld syndrome with common single atrium"],"prefix":"10.1136","volume":"14","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-3726-4889","authenticated-orcid":false,"given":"Kesar","family":"Prajapati","sequence":"first","affiliation":[{"name":"Medicine, Baroda Medical College, Vadodara, Gujarat, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jaya","family":"Pathak","sequence":"additional","affiliation":[{"name":"Medicine, Baroda Medical College, Vadodara, Gujarat, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Vikranti","family":"Sailor","sequence":"additional","affiliation":[{"name":"Medicine department, Baroda Medical College, Vadodara, Gujarat, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1925-0563","authenticated-orcid":false,"given":"Parth","family":"Adrejiya","sequence":"additional","affiliation":[{"name":"Medicine department, Baroda Medical College, Vadodara, Gujarat, India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2021,3,24]]},"reference":[{"key":"2025082708454333000_14.3.e239663.1","doi-asserted-by":"publisher","DOI":"10.4103\/0974-620X.60017"},{"key":"2025082708454333000_14.3.e239663.2","doi-asserted-by":"publisher","DOI":"10.1007\/s00247-013-2709-y"},{"key":"2025082708454333000_14.3.e239663.3","first-page":"866","article-title":"Ellis van Creveld syndrome","volume":"41","author":"Haque","year":"2004","journal-title":"Indian Pediatr"},{"key":"2025082708454333000_14.3.e239663.4","doi-asserted-by":"publisher","DOI":"10.1086\/368063"},{"key":"2025082708454333000_14.3.e239663.5","unstructured":"Ortega J , Ferrer J , Fernandez A . 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