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He was diagnosed with HUVS after a 6-month period of bilateral scleritis, vestibulitis, significant weight loss, mononeuritis multiplex and recurrent urticarial vasculitis with pronounced persistent hypocomplementemia and the presence of anti-C1q antibodies. Disease control was eventually obtained with mycophenolate and prednisolone.<\/jats:p>","DOI":"10.1136\/bcr-2020-240041","type":"journal-article","created":{"date-parts":[[2021,5,10]],"date-time":"2021-05-10T13:36:17Z","timestamp":1620653777000},"page":"e240041","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Hypocomplementemic urticarial vasculitis syndrome presenting with bilateral scleritis"],"prefix":"10.1136","volume":"14","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6128-683X","authenticated-orcid":false,"given":"Ella Claire","family":"Berry","sequence":"first","affiliation":[{"name":"Canberra Health Services Library, ACT Government, Garren, Australian Capital Territory, Australia"},{"name":"Ophthalmology Unit, Canberra Health Services, Garran, Australian Capital Territory, 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