{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,6]],"date-time":"2026-02-06T22:32:28Z","timestamp":1770417148734,"version":"3.49.0"},"reference-count":5,"publisher":"BMJ","issue":"5","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2021,5,4]]},"published-print":{"date-parts":[[2021,5]]},"abstract":"<jats:p>We report a case of a 16-year-old adolescent male born with univentricular congenital cyanotic heart disease (CCHD) who was diagnosed with an incidental paraganglioma while awaiting a cardiac transplant. The coexistence of paraganglioma and univentricular CCHD is very rare, with no previous cases described in the literature of a patient concurrently requiring a cardiac transplant. The complex physiology associated with a common atrium, common ventricle, aortopulmonary lung perfusion and a hypoplastic left lung rendered our patient extremely vulnerable to catecholamine-mediated effects of preload, contractility and afterload. The interactions and interdependence between these systems provided unique difficulties for perioperative management with serious implications for prospective cardiac transplant.<\/jats:p>","DOI":"10.1136\/bcr-2021-241804","type":"journal-article","created":{"date-parts":[[2021,5,25]],"date-time":"2021-05-25T12:33:24Z","timestamp":1621946004000},"page":"e241804","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Paraganglioma in an adolescent awaiting a cardiac transplant due to unrepaired congenital cyanotic heart disease and a univentricular heart: the first reported case"],"prefix":"10.1136","volume":"14","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9124-5297","authenticated-orcid":false,"given":"Conor","family":"Doyle","sequence":"first","affiliation":[{"name":"Cardiology, Mater Misericordiae University Hospital, Dublin, Ireland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jarlath","family":"Bolger","sequence":"additional","affiliation":[{"name":"General Surgery, Mater Misericordiae University Hospital, Dublin, Ireland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"John B","family":"Conneely","sequence":"additional","affiliation":[{"name":"Department of Hepatobiliary Surgery, Mater Misericordiae University Hospital, Dublin, Ireland"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kevin P","family":"Walsh","sequence":"additional","affiliation":[{"name":"Department of Cardiology, Mater Misericordiae University Hospital, Dublin, Ireland"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2021,5,25]]},"reference":[{"key":"2025082723055693000_14.5.e241804.1","doi-asserted-by":"publisher","DOI":"10.1016\/j.beem.2010.10.004"},{"key":"2025082723055693000_14.5.e241804.2","doi-asserted-by":"publisher","DOI":"10.1210\/jc.2014-3863"},{"key":"2025082723055693000_14.5.e241804.3","doi-asserted-by":"publisher","DOI":"10.1016\/S0002-9149(97)00544-4"},{"key":"2025082723055693000_14.5.e241804.4","doi-asserted-by":"publisher","DOI":"10.1053\/jcan.2002.128436"},{"key":"2025082723055693000_14.5.e241804.5","doi-asserted-by":"crossref","first-page":"728","DOI":"10.1111\/j.1399-3046.2011.01561.x","article-title":"Red blood cell transfusions in children awaiting heart transplantation","volume":"15","author":"Mahle","year":"2011","journal-title":"Pediatr Transplant"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2021-241804","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T06:06:04Z","timestamp":1756361164000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2021-241804"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2021,5]]},"references-count":5,"journal-issue":{"issue":"5","published-online":{"date-parts":[[2021,5,25]]},"published-print":{"date-parts":[[2021,5]]}},"alternative-id":["10.1136\/bcr-2021-241804"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2021-241804","relation":{},"ISSN":["1757-790X"],"issn-type":[{"value":"1757-790X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2021,5]]}}}