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We provide an overview of the literature and highlight the need to consider appendiceal mucinous neoplasm as a differential in the management of spontaneous right iliac fossa collections and fistulae.<\/jats:p>","DOI":"10.1136\/bcr-2021-244546","type":"journal-article","created":{"date-parts":[[2021,8,26]],"date-time":"2021-08-26T12:46:00Z","timestamp":1629981960000},"page":"e244546","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":3,"title":["Enterocutaneous fistula resulting from the drainage of a contained appendiceal perforation secondary to a partially obstructing low-grade appendiceal mucinous neoplasm"],"prefix":"10.1136","volume":"14","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9772-4571","authenticated-orcid":false,"given":"Ryan","family":"Cohen","sequence":"first","affiliation":[{"name":"School of Biomedical Sciences, The University of Western Australia, Perth, Western Australia, Australia"},{"name":"School of Medicine, The University of Notre Dame, Fremantle, Western Australia, Australia"},{"name":"Colorectal Surgery, St John of God Health Care Inc, Perth, Western Australia, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Katie","family":"McKean","sequence":"additional","affiliation":[{"name":"Colorectal Surgery, St John of God Health Care Inc, Perth, Western Australia, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stephanie","family":"Chetrit","sequence":"additional","affiliation":[{"name":"Colorectal Surgery, St John of God Health Care Inc, Perth, Western Australia, Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2021,8,26]]},"reference":[{"key":"2025082709430334000_14.8.e244546.1","doi-asserted-by":"crossref","first-page":"569","DOI":"10.1097\/COC.0000000000000210","article-title":"Incidence and survival of appendiceal mucinous neoplasms","volume":"40","author":"Shaib","year":"2017","journal-title":"Am J Clin Oncol"},{"key":"2025082709430334000_14.8.e244546.2","doi-asserted-by":"publisher","DOI":"10.1097\/PAS.0000000000000535"},{"key":"2025082709430334000_14.8.e244546.3","doi-asserted-by":"crossref","first-page":"847","DOI":"10.1111\/his.13324","article-title":"The histopathological classification, diagnosis and differential diagnosis of mucinous appendiceal neoplasms, appendiceal adenocarcinomas and pseudomyxoma peritonei","volume":"71","author":"Carr","year":"2017","journal-title":"Histopathology"},{"key":"2025082709430334000_14.8.e244546.4","doi-asserted-by":"publisher","DOI":"10.1097\/00000478-200308000-00006"},{"key":"2025082709430334000_14.8.e244546.5","doi-asserted-by":"publisher","DOI":"10.1016\/j.ejso.2007.04.002"},{"key":"2025082709430334000_14.8.e244546.6","doi-asserted-by":"publisher","DOI":"10.1001\/archsurg.138.6.585"},{"key":"2025082709430334000_14.8.e244546.7","doi-asserted-by":"publisher","DOI":"10.1148\/rg.233025134"},{"key":"2025082709430334000_14.8.e244546.8","doi-asserted-by":"crossref","first-page":"1753","DOI":"10.1245\/s10434-020-08316-w","article-title":"The Chicago consensus on peritoneal surface malignancies: management of appendiceal neoplasms","volume":"27","year":"2020","journal-title":"Ann Surg Oncol"},{"key":"2025082709430334000_14.8.e244546.9","doi-asserted-by":"crossref","first-page":"S67","DOI":"10.1038\/modpathol.2014.129","article-title":"Mucinous epithelial neoplasms of the appendix and pseudomyxoma peritonei","volume":"28 Suppl 1","author":"Misdraji","year":"2015","journal-title":"Mod Pathol"},{"key":"2025082709430334000_14.8.e244546.10","doi-asserted-by":"crossref","first-page":"2068","DOI":"10.1007\/s11605-009-0922-7","article-title":"How I do it: gastrointestinal cutaneous fistulas","volume":"13","author":"Osborn","year":"2009","journal-title":"J Gastrointest Surg"},{"key":"2025082709430334000_14.8.e244546.11","doi-asserted-by":"publisher","DOI":"10.1016\/j.jamcollsurg.2009.05.025"},{"key":"2025082709430334000_14.8.e244546.12","first-page":"267","article-title":"Cystadenocarcinoma of appendix with cutaneous fistula - 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