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In this report, we review the pathophysiology, comorbidities and diagnostic workup in patients presenting with left ventricular non-compaction in the context of dystrophinopathy. Ultimately, we suggest the consideration of rare cardiomyopathies in all patients presenting with neuromuscular syndromes and vice versa.<\/jats:p>","DOI":"10.1136\/bcr-2021-244745","type":"journal-article","created":{"date-parts":[[2021,11,11]],"date-time":"2021-11-11T12:31:09Z","timestamp":1636633869000},"page":"e244745","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Non-compaction cardiomyopathy, Becker muscular dystrophy, neuropathy and recurrent syncope"],"prefix":"10.1136","volume":"14","author":[{"given":"Love","family":"Shah","sequence":"first","affiliation":[{"name":"Internal Medicine, University of Saskatchewan, Saskatoon, Saskatchewan, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ingrid","family":"Tam","sequence":"additional","affiliation":[{"name":"Pathology and Lab Medicine, University of Saskatchewan College of Medicine, Saskatoon, Saskatchewan, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shravan","family":"Nosib","sequence":"additional","affiliation":[{"name":"Cardiology, University of Saskatchewan, Saskatoon, Saskatchewan, Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2021,11,11]]},"reference":[{"key":"2025082800231381000_14.11.e244745.1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.c.31366"},{"key":"2025082800231381000_14.11.e244745.2","doi-asserted-by":"publisher","DOI":"10.1093\/eurheartj\/ehq508"},{"key":"2025082800231381000_14.11.e244745.3","doi-asserted-by":"publisher","DOI":"10.1016\/S0735-1097(00)00755-5"},{"key":"2025082800231381000_14.11.e244745.4","doi-asserted-by":"publisher","DOI":"10.1016\/j.jacc.2016.05.096"},{"key":"2025082800231381000_14.11.e244745.5","doi-asserted-by":"publisher","DOI":"10.1038\/nrcardio.2016.207"},{"key":"2025082800231381000_14.11.e244745.6","doi-asserted-by":"publisher","DOI":"10.1007\/BF00858726"},{"key":"2025082800231381000_14.11.e244745.7","doi-asserted-by":"crossref","unstructured":"Hoffman EP . 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