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Following this, we present a comprehensive review of the literature.<\/jats:p>","DOI":"10.1136\/bcr-2022-250825","type":"journal-article","created":{"date-parts":[[2022,9,28]],"date-time":"2022-09-28T11:25:27Z","timestamp":1664364327000},"page":"e250825","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Recurrent haemoptysis: a rare diagnosis of kaposiform lymphangiomatosis and review of literature"],"prefix":"10.1136","volume":"15","author":[{"given":"Roukhama","family":"Fedidat","sequence":"first","affiliation":[{"name":"Internal Medicine, Hadassah Medical Center, Jerusalem, Israel"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Anna","family":"Elia","sequence":"additional","affiliation":[{"name":"Pathology, Hadassah Medical Center, Jerusalem, Israel"},{"name":"Faculty of Medicine, Hebrew University, Jerusalem, Israel"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alon","family":"Hershko","sequence":"additional","affiliation":[{"name":"Faculty of Medicine, Hebrew University, Jerusalem, Israel"},{"name":"Internal Medicine & Clinical Immunology, Hadassah Medical Center, Jerusalem, Israel"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6122-1988","authenticated-orcid":false,"given":"Zvi","family":"Fridlender","sequence":"additional","affiliation":[{"name":"Faculty of Medicine, Hebrew University, Jerusalem, Israel"},{"name":"Internal Medicine & Pulmonology, Hadassah Medical Center, Jerusalem, Israel"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2022,9,28]]},"reference":[{"key":"2025082712495043000_15.9.e250825.1","doi-asserted-by":"publisher","DOI":"10.1542\/peds.2014-3673"},{"key":"2025082712495043000_15.9.e250825.2","unstructured":"International Society for the study of vascular anomalies: ISSVA classification for vascular anomalies (Approved at the may 2018 General assembly in Amsterdam, the Netherlands). 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Kaposiform lymangiomatosis: a new entity distinct from generalized lymphatic anomaly, kaposiform hemangioendothelioma, lymphedema associated angiosaroma, and lymphangioma-like Kaposi sarcoma. platform presentation at the International Society of vascular anomalies meeting 2012, Malmo, Sweden."},{"key":"2025082712495043000_15.9.e250825.14","first-page":"269","article-title":"Kaposiform lymphangiomatosis (KLA): an aggressive variant of lymphangiomatosis [abstract]","volume":"84","author":"Debelenko","year":"2004","journal-title":"Lab Invest"},{"key":"2025082712495043000_15.9.e250825.15","first-page":"457","article-title":"Kaposiform haemangioendothelioma: clinical features, complications and risk factors for Kasabach-Merritt phenomenon","volume":"179","author":"Ji","year":"2018","journal-title":"Br J Dermatol"},{"key":"2025082712495043000_15.9.e250825.16","doi-asserted-by":"crossref","DOI":"10.1186\/s13023-021-01893-3","article-title":"Sirolimus in the treatment of kaposiform lymphangiomatosis","volume":"16","author":"Zhou","year":"2021","journal-title":"Orphanet J Rare Dis"},{"key":"2025082712495043000_15.9.e250825.17","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.25914"},{"key":"2025082712495043000_15.9.e250825.18","doi-asserted-by":"crossref","first-page":"901","DOI":"10.1002\/pbc.25278","article-title":"Kaposiform lymphangiomatosis: unifying features of a heterogeneous disorder","volume":"62","author":"Fernandes","year":"2015","journal-title":"Pediatr Blood Cancer"},{"key":"2025082712495043000_15.9.e250825.19","doi-asserted-by":"publisher","DOI":"10.1055\/s-0036-1593383"},{"key":"2025082712495043000_15.9.e250825.20","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.25422"},{"key":"2025082712495043000_15.9.e250825.21","doi-asserted-by":"publisher","DOI":"10.1542\/peds.2015-4450"},{"key":"2025082712495043000_15.9.e250825.22","doi-asserted-by":"crossref","DOI":"10.1002\/pbc.27790","article-title":"Signaling pathways and inhibitors of cells from patients with kaposiform lymphangiomatosis","volume":"66","author":"Boscolo","year":"2019","journal-title":"Pediatr Blood Cancer"},{"key":"2025082712495043000_15.9.e250825.23","doi-asserted-by":"publisher","DOI":"10.1038\/s41436-018-0390-0"},{"key":"2025082712495043000_15.9.e250825.24","doi-asserted-by":"crossref","DOI":"10.1186\/s13023-019-1191-5","article-title":"Detection of NRAS mutation in cell-free DNA biological fluids from patients with kaposiform lymphangiomatosis","volume":"14","author":"Ozeki","year":"2019","journal-title":"Orphanet J Rare Dis"},{"key":"2025082712495043000_15.9.e250825.25","doi-asserted-by":"publisher","DOI":"10.15252\/emmm.202012324"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2022-250825","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,8,27]],"date-time":"2025-08-27T19:50:00Z","timestamp":1756324200000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2022-250825"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,9]]},"references-count":25,"journal-issue":{"issue":"9","published-online":{"date-parts":[[2022,9,28]]},"published-print":{"date-parts":[[2022,9]]}},"alternative-id":["10.1136\/bcr-2022-250825"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2022-250825","relation":{},"ISSN":["1757-790X"],"issn-type":[{"type":"electronic","value":"1757-790X"}],"subject":[],"published":{"date-parts":[[2022,9]]}}}