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This case report highlights his management and discusses these conditions\u2019 pathophysiology and future management.<\/jats:p>","DOI":"10.1136\/bcr-2022-252637","type":"journal-article","created":{"date-parts":[[2023,1,31]],"date-time":"2023-01-31T10:01:33Z","timestamp":1675159293000},"page":"e252637","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":5,"title":["Inflammatory epilepsy (FIRES) and haemophagocytic lymphohistiocytosis (HLH): an adult case"],"prefix":"10.1136","volume":"16","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-1565-5064","authenticated-orcid":false,"given":"Ian","family":"Kam","sequence":"first","affiliation":[{"name":"Neurology, Royal Perth Hospital, Perth, Western Australia, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"David","family":"Prentice","sequence":"additional","affiliation":[{"name":"Neurology, Perron Institute for Neurological and Translational Science, Nedlands, Western Australia, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lay Kun","family":"Kho","sequence":"additional","affiliation":[{"name":"Neurology, Royal Perth Hospital, Perth, Western Australia, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ferry","family":"Dharsono","sequence":"additional","affiliation":[{"name":"The Neurological Intervention & Imaging Service of Western Australia, Sir Charles Gairdner Hospital, Nedlands, Western Australia, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2023,1,31]]},"reference":[{"key":"2025082804285399000_16.1.e252637.1","doi-asserted-by":"publisher","DOI":"10.1111\/epi.14022"},{"key":"2025082804285399000_16.1.e252637.2","doi-asserted-by":"crossref","first-page":"22","DOI":"10.1002\/epi4.12454","article-title":"Super refractory status in a case of febrile infection-related epilepsy syndrome due to hemophagocytic lymphocytic histiocytosis","volume":"6","author":"Meenakshi-Sundaram","year":"2021","journal-title":"Epilepsia Open"},{"key":"2025082804285399000_16.1.e252637.3","doi-asserted-by":"crossref","first-page":"1753","DOI":"10.1111\/epi.14524","article-title":"Fueling the fires: hemophagocytic lymphohistiocytosis in febrile infection-related epilepsy syndrome","volume":"59","author":"Farias-Moeller","year":"2018","journal-title":"Epilepsia"},{"key":"2025082804285399000_16.1.e252637.4","doi-asserted-by":"crossref","first-page":"585","DOI":"10.1111\/epi.14684","article-title":"The spectrum of neuroimaging findings in febrile infection-related epilepsy syndrome (fires): a literature review","volume":"60","author":"Culleton","year":"2019","journal-title":"Epilepsia"},{"key":"2025082804285399000_16.1.e252637.5","doi-asserted-by":"crossref","first-page":"111","DOI":"10.3389\/fneur.2017.00111","article-title":"New-onset refractory status epilepticus with claustrum damage: definition of the clinical and neuroimaging features","volume":"8","author":"Meletti","year":"2017","journal-title":"Front Neurol"},{"key":"2025082804285399000_16.1.e252637.6","doi-asserted-by":"publisher","DOI":"10.1007\/s00296-020-04636-y"},{"key":"2025082804285399000_16.1.e252637.7","doi-asserted-by":"publisher","DOI":"10.1038\/nrneurol.2010.178"},{"key":"2025082804285399000_16.1.e252637.8","doi-asserted-by":"crossref","unstructured":"Lin Lin Lee V , Shaikh MF . 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