{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,13]],"date-time":"2026-10-13T22:42:57Z","timestamp":1791931377555,"version":"4.3.4"},"reference-count":31,"publisher":"BMJ","issue":"7","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2023,7,7]]},"published-print":{"date-parts":[[2023,7]]},"abstract":"<jats:p>Angiosarcoma is an incredibly rare type of malignancy, accounting for only 1%\u20132% of all soft-tissue sarcomas globally. It is clinically, pathologically and radiologically difficult to diagnose angiosarcoma owing to its varied presentation with little or no well-defined imaging findings.<\/jats:p>\n               <jats:p>Kasabach-Merritt syndrome is also a lesser-heard entity which carries extremely poor prognosis. It is primarily seen in infants with vascular malformations and in kaposiform haemangioendothelioma. It is a condition of consumptive coagulopathy and only few of the cases have been reported so far in the adults with a background of angiosarcoma.<\/jats:p>\n               <jats:p>This report presents the case of a male in his 70s who was diagnosed with metastatic angiosarcoma and experienced a complicated disease course due to Kasabach-Merritt syndrome.<\/jats:p>","DOI":"10.1136\/bcr-2023-255134","type":"journal-article","created":{"date-parts":[[2023,7,27]],"date-time":"2023-07-27T11:35:10Z","timestamp":1690457710000},"page":"e255134","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":1,"title":["Recurrent metastatic angiosarcoma presenting as Kasabach-Merritt syndrome"],"prefix":"10.1136","volume":"16","author":[{"given":"Jeyhan Boman","family":"Dhabhar","sequence":"first","affiliation":[{"name":"Medical Oncology, PD Hinduja National Hospital and Medical Research Centre, Mumbai, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5804-9948","authenticated-orcid":false,"given":"Varshil","family":"Mehta","sequence":"additional","affiliation":[{"name":"Medicine, Northwick Park Hospital, Harrow, UK"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2023,7,27]]},"reference":[{"key":"2025082722345431000_16.7.e255134.1","doi-asserted-by":"publisher","DOI":"10.1002\/1097-0142(19950215)75:4<989::AID-CNCR2820750414>3.0.CO;2-K"},{"key":"2025082722345431000_16.7.e255134.2","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMra041866"},{"key":"2025082722345431000_16.7.e255134.3","doi-asserted-by":"crossref","first-page":"828","DOI":"10.1055\/s-0037-1616139","article-title":"Disseminated intravascular coagulation in solid tumors: clinical and pathologic study","volume":"86","author":"Sallah","year":"2001","journal-title":"Thromb Haemost"},{"key":"2025082722345431000_16.7.e255134.4","doi-asserted-by":"publisher","DOI":"10.1016\/S1470-2045(10)70023-1"},{"key":"2025082722345431000_16.7.e255134.5","doi-asserted-by":"crossref","first-page":"273","DOI":"10.1177\/000331979704800312","article-title":"Interferon Alpha-2A therapy for disseminated intravascular coagulation in a patient with blue rubber Bleb Nevus syndrome. 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