{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,6]],"date-time":"2026-01-06T13:58:46Z","timestamp":1767707926727,"version":"3.44.0"},"reference-count":35,"publisher":"BMJ","issue":"1","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2023,12,27]]},"published-print":{"date-parts":[[2024,1]]},"abstract":"<jats:p>A man in his 40s presented to an emergency department after experiencing worsening abdominal pain for 2\u2009days. Contrast-enhanced CT of the abdomen and pelvis revealed circumferential mural thickening and luminal narrowing of the distal ileum and upstream dilatation of the small intestine, indicating small intestine obstruction. This prompted emergency laparotomy, where two lesions in the distal ileum were identified as the source of his bowel obstruction and resected. Immunohistochemistry of the resected segment revealed a primary small intestine angiosarcoma acting positively for vascular markers ERG and CD31. A subsequent positron emission tomography (PET) scan revealed positive mediastinal metastatic lymphadenopathy without organ metastases.<\/jats:p>\n               <jats:p>Following his surgery, the patient recovered well and was promptly referred to an oncology unit at a specialised health centre for further treatment. Primary small intestine angiosarcoma is a rare entity in which patients present with non-specific symptoms requiring prompt tissue diagnosis to facilitate multidisciplinary management.<\/jats:p>","DOI":"10.1136\/bcr-2023-255424","type":"journal-article","created":{"date-parts":[[2024,1,30]],"date-time":"2024-01-30T21:55:23Z","timestamp":1706651723000},"page":"e255424","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":1,"title":["Primary small intestine angiosarcoma mimicking Crohn\u2019s disease"],"prefix":"10.1136","volume":"17","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-9666-5853","authenticated-orcid":false,"given":"Prasanthan","family":"Thaveenthiran","sequence":"first","affiliation":[{"name":"General Surgery, Monash Health, Clayton, Victoria, Australia"},{"name":"Trauma, National Trauma Research Institute, The Alfred Hospital, Melbourne, Victoria, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lily","family":"Bae","sequence":"additional","affiliation":[{"name":"General Surgery, Monash Health, Clayton, Victoria, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Chandika","family":"Wewelwala","sequence":"additional","affiliation":[{"name":"General Surgery, Monash Health, Clayton, Victoria, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kevin","family":"Zhou","sequence":"additional","affiliation":[{"name":"Radiology, Monash Health, Clayton, Victoria, Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2024,1,30]]},"reference":[{"key":"2025082800574079000_17.1.e255424.1","doi-asserted-by":"crossref","first-page":"817","DOI":"10.1159\/000485345","article-title":"Clinical characteristics and prognostic factors of small intestine angiosarcoma: a retrospective clinical analysis of 66 cases","volume":"44","author":"Li","year":"2017","journal-title":"Cell Physiol Biochem"},{"key":"2025082800574079000_17.1.e255424.2","doi-asserted-by":"crossref","first-page":"561","DOI":"10.3748\/wjg.v29.i3.561","article-title":"Small intestinal angiosarcoma on clinical presentation, diagnosis, management and prognosis: a case report and review of the literature","volume":"29","author":"Ma","year":"2023","journal-title":"World J Gastroenterol"},{"key":"2025082800574079000_17.1.e255424.3","doi-asserted-by":"crossref","first-page":"294","DOI":"10.14740\/jocmr3153w","article-title":"Primary small intestinal angiosarcoma: epidemiology","volume":"10","author":"Nai","year":"2018","journal-title":"J Clin Med Res"},{"key":"2025082800574079000_17.1.e255424.4","doi-asserted-by":"crossref","unstructured":"Rami Reddy SR , Cappell MS . 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