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This case highlights the importance of early diagnosis, multidisciplinary care and vigilant follow-up in achieving favourable outcomes in rare congenital conditions.<\/jats:p>","DOI":"10.1136\/bcr-2024-261911","type":"journal-article","created":{"date-parts":[[2025,3,7]],"date-time":"2025-03-07T13:45:36Z","timestamp":1741355136000},"page":"e261911","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Overcoming odds: neonatal survival in absent right main pulmonary artery with unilateral right pulmonary hypoplasia"],"prefix":"10.1136","volume":"18","author":[{"given":"Debajyoti","family":"Banerjee","sequence":"first","affiliation":[{"name":"Paediatrics, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Brajendra","family":"Singh","sequence":"additional","affiliation":[{"name":"Neonatology, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9413-4696","authenticated-orcid":false,"given":"Saikat","family":"Patra","sequence":"additional","affiliation":[{"name":"Neonatology, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Girish","family":"Gupta","sequence":"additional","affiliation":[{"name":"Neonatology, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2025,3,7]]},"reference":[{"key":"2025082708461773000_18.3.e261911.1","doi-asserted-by":"publisher","DOI":"10.4103\/0970-2113.44215"},{"key":"2025082708461773000_18.3.e261911.2","doi-asserted-by":"publisher","DOI":"10.1046\/j.1469-0705.2000.00252.x"},{"key":"2025082708461773000_18.3.e261911.3","article-title":"Infant with Clinical Evidence of Pulmonary Hypoplasia: A Case Report","volume":"9","author":"Glasberg","year":"2017","journal-title":"Cureus"},{"key":"2025082708461773000_18.3.e261911.4","doi-asserted-by":"publisher","DOI":"10.1016\/j.jcma.2011.12.004"},{"key":"2025082708461773000_18.3.e261911.5","doi-asserted-by":"crossref","first-page":"667","DOI":"10.1038\/sj.jp.7211156","article-title":"Primary unilateral pulmonary hypoplasia: neonate through early childhood - case report, radiographic diagnosis and review of the literature","volume":"24","author":"Abrams","year":"2004","journal-title":"J Perinatol"},{"key":"2025082708461773000_18.3.e261911.6","doi-asserted-by":"publisher","DOI":"10.1016\/j.pedneo.2016.04.001"},{"key":"2025082708461773000_18.3.e261911.7","article-title":"A Rare Case of Lung Hypoplasia in a 1-Year-Old Girl","volume":"14","author":"Rashed","year":"2022","journal-title":"Cureus"},{"key":"2025082708461773000_18.3.e261911.8","doi-asserted-by":"crossref","unstructured":"Wallace MJ , Hooper SB , Harding R . 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