{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,16]],"date-time":"2026-06-16T17:17:36Z","timestamp":1781630256478,"version":"3.54.5"},"reference-count":16,"publisher":"BMJ","issue":"7","license":[{"start":{"date-parts":[[2025,7,17]],"date-time":"2025-07-17T00:00:00Z","timestamp":1752710400000},"content-version":"unspecified","delay-in-days":16,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2025,6,30]]},"published-print":{"date-parts":[[2025,7]]},"abstract":"<jats:p>Adult-onset Still\u2019s disease is a rare systemic autoinflammatory condition of unknown aetiology. It is a diagnosis of exclusion based primarily on clinical features and non-specific laboratory findings using either the Yamaguchi or Fautrel criteria. Here, we present a case of atypical adult-onset Still\u2019s disease in a young man with twice-daily fevers, night sweats and evanescent rash on his face but not enough features to meet the Yamaguchi or Fautrel criteria after extensive (but unrevealing) infectious, autoimmune and malignancy workups. He responded well to corticosteroid therapy with periodic relapses while transitioning to anti-IL1 therapy for 8\u2009months. At a 2-year follow-up, he now remains symptom-free after stopping anti-IL1 therapy for over a year.<\/jats:p>","DOI":"10.1136\/bcr-2025-267006","type":"journal-article","created":{"date-parts":[[2025,7,18]],"date-time":"2025-07-18T10:00:26Z","timestamp":1752832826000},"page":"e267006","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":2,"title":["Atypical adult-onset Still\u2019s disease that fails to meet Yamaguchi and Fautrel criteria"],"prefix":"10.1136","volume":"18","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0377-3207","authenticated-orcid":false,"given":"Andrew C","family":"Kelleher","sequence":"first","affiliation":[{"name":"Medicine, New York University Grossman School of Medicine, New York, New York, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jonathan","family":"Samuels","sequence":"additional","affiliation":[{"name":"Medicine, NYU Langone Health, New York, New York, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2025,7,18]]},"reference":[{"key":"2025082712375655000_18.7.e267006.1","doi-asserted-by":"crossref","first-page":"50","DOI":"10.1186\/s13023-023-02651-3","article-title":"Increased incidence of adult-onset Still\u2019s disease in association with COVID-19 vaccination and SARS-CoV-2 infection","volume":"18","author":"Gottschalk","year":"2023","journal-title":"Orphanet J Rare Dis"},{"key":"2025082712375655000_18.7.e267006.2","first-page":"424","article-title":"Preliminary criteria for classification of adult Still\u2019s disease","volume":"19","author":"Yamaguchi","year":"1992","journal-title":"J Rheumatol"},{"key":"2025082712375655000_18.7.e267006.3","doi-asserted-by":"publisher","DOI":"10.1097\/00005792-200205000-00003"},{"key":"2025082712375655000_18.7.e267006.4","doi-asserted-by":"crossref","DOI":"10.1093\/ofid\/ofac396","article-title":"Geographic Influence Upon Noninfectious 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