{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,7]],"date-time":"2026-01-07T17:28:05Z","timestamp":1767806885947,"version":"3.49.0"},"reference-count":12,"publisher":"BMJ","issue":"1","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2025,12,26]]},"published-print":{"date-parts":[[2026,1]]},"abstract":"<jats:p>Unilateral absence of pulmonary artery (UAPA) is a rare congenital abnormality that occurs during embryonic development. Isolated UAPA has a prevalence of about 1 in 200 000. The clinical presentation varies based on age, but manifestations include recurrent pneumonia, haemoptysis, pulmonary hypertension or an incidental finding, among others. Here, we present two adult patients with isolated UAPA who were diagnosed with pulmonary hypertension and have been medically managed at our institution.<\/jats:p>","DOI":"10.1136\/bcr-2025-269028","type":"journal-article","created":{"date-parts":[[2026,1,7]],"date-time":"2026-01-07T12:45:36Z","timestamp":1767789936000},"page":"e269028","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Unilateral absence of pulmonary artery presenting with pulmonary hypertension in two adults"],"prefix":"10.1136","volume":"19","author":[{"given":"Vandana Kavita","family":"Seeram","sequence":"first","affiliation":[{"name":"Pulmonary\/Critical care, University of Florida, College of Medicine-Jacksonville, Jacksonville, Florida, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-5165-2768","authenticated-orcid":false,"given":"Leela Krishna Teja","family":"Boppana","sequence":"additional","affiliation":[{"name":"Pulmonary\/Critical care, University of Florida, College of Medicine-Jacksonville, Jacksonville, Florida, USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[2026,1,7]]},"reference":[{"key":"2026010704453370000_19.1.e269028.1","doi-asserted-by":"publisher","DOI":"10.1378\/chest.122.4.1471"},{"key":"2026010704453370000_19.1.e269028.2","doi-asserted-by":"publisher","DOI":"10.1510\/icvts.2010.250795A"},{"key":"2026010704453370000_19.1.e269028.3","doi-asserted-by":"publisher","DOI":"10.2214\/ajr.179.5.1791253"},{"key":"2026010704453370000_19.1.e269028.4","doi-asserted-by":"publisher","DOI":"10.1016\/j.acvd.2013.05.004"},{"key":"2026010704453370000_19.1.e269028.5","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1186\/s43168-023-00184-8","article-title":"Isolated unilateral absence of pulmonary artery- an unusual cause of hemoptysis: a case report","volume":"17","author":"Khaladkar","year":"2023","journal-title":"Egypt J Bronchol"},{"key":"2026010704453370000_19.1.e269028.6","first-page":"238","article-title":"Unilateral absent pulmonary artery in an adult - A diagnostic and therapeutic challenge","volume":"22","author":"Seedat","year":"2017","journal-title":"Respir Med Case Rep"},{"key":"2026010704453370000_19.1.e269028.7","doi-asserted-by":"crossref","first-page":"4988","DOI":"10.21037\/jtd.2017.11.49","article-title":"Isolated unilateral absence of pulmonary artery in adulthood: a clinical analysis of 65 cases from a case series and systematic review","volume":"9","author":"Wang","year":"2017","journal-title":"J Thorac Dis"},{"key":"2026010704453370000_19.1.e269028.8","doi-asserted-by":"crossref","DOI":"10.1177\/2050313X221127667","article-title":"Pulmonary hypertension in an adult with unilateral absence of left pulmonary artery","volume":"10","author":"Ghazarian","year":"2022","journal-title":"SAGE Open Med Case Rep"},{"key":"2026010704453370000_19.1.e269028.9","doi-asserted-by":"crossref","first-page":"86","DOI":"10.1016\/j.rmed.2019.07.011","article-title":"Developmental lung anomalies in adults: A pictorial review","volume":"155","author":"Cherian","year":"2019","journal-title":"Respir Med"},{"key":"2026010704453370000_19.1.e269028.10","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.00879-2022"},{"key":"2026010704453370000_19.1.e269028.11","first-page":"24","article-title":"Isolated right pulmonary artery discontinuity","volume":"2","author":"Turner","year":"2000","journal-title":"Images Paediatr Cardiol"},{"key":"2026010704453370000_19.1.e269028.12","doi-asserted-by":"publisher","DOI":"10.1161\/CIRCULATIONAHA.108.777698"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2025-269028","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,1,7]],"date-time":"2026-01-07T12:45:37Z","timestamp":1767789937000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2025-269028"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,1]]},"references-count":12,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2026,1,7]]},"published-print":{"date-parts":[[2026,1]]}},"alternative-id":["10.1136\/bcr-2025-269028"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2025-269028","relation":{},"ISSN":["1757-790X"],"issn-type":[{"value":"1757-790X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,1]]}}}