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B-scan ultrasonography demonstrated a bi-lobulated retinal lesion with calcifications extending into the anterior hyaloid to the lens. Since the findings were highly suggestive of retinoblastoma, urgent MRI was arranged which demonstrated a right globe intraocular mass with no optic nerve or intracranial extension. The tumour was classified as Group E retinoblastoma, based on the International Intraocular Retinoblastoma Classification (IIRC) classification system. She underwent right eye enucleation and was fitted with a prosthesis. At nearly 1 year of follow-up, the patient remains clinically well and undergoes regular follow-ups with our retinoblastoma service<\/jats:p>","DOI":"10.1136\/bcr-2025-270498","type":"journal-article","created":{"date-parts":[[2026,7,22]],"date-time":"2026-07-22T14:20:19Z","timestamp":1784730019000},"page":"e270498","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Retinoblastoma presenting as congenital glaucoma"],"prefix":"10.1136","volume":"19","author":[{"ORCID":"https:\/\/orcid.org\/0009-0001-8602-6011","authenticated-orcid":false,"given":"Reem","family":"AlShimali","sequence":"first","affiliation":[{"name":"Ministry of Health, Shuwaikh, Kuwait City, Kuwait"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rawan","family":"AlShemali","sequence":"additional","affiliation":[{"name":"Ministry of Health, Shuwaikh, Kuwait City, Kuwait"},{"name":"AlBahar Eye Center, Ibn Sina Hospital, Shuwaikh, Kuwait 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