{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,21]],"date-time":"2026-09-21T15:02:31Z","timestamp":1790002951270,"version":"4.0.1"},"reference-count":11,"publisher":"BMJ","issue":"9","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["BMJ Case Rep"],"accepted":{"date-parts":[[2026,8,2]]},"published-print":{"date-parts":[[2026,9]]},"abstract":"<jats:p>A boy in early adolescence was diagnosed with left-sided congenital pulmonary airway malformation (CPAM) at birth and remained asymptomatic until early adolescence, when he presented with dry cough, right-sided chest pain and breathlessness on exertion. Imaging showed right-sided pleural effusion with pulmonary nodules and skeletal metastases. Thoracoscopic biopsy confirmed pleuropulmonary blastoma (PPB) of type III. Despite receiving aggressive chemotherapy, the disease progressed rapidly and the outcome was fatal.<\/jats:p>\n                  <jats:p>\n                    This case highlights the diagnostic challenges of advanced PPB in adolescents and the poor prognosis once the disease metastasises. It also emphasises the importance of timely surgical management of CPAM and the need to consider screening in individuals with a family history of CPAM or\n                    <jats:italic>DICER1<\/jats:italic>\n                    mutations.\n                  <\/jats:p>","DOI":"10.1136\/bcr-2026-274209","type":"journal-article","created":{"date-parts":[[2026,9,21]],"date-time":"2026-09-21T14:16:05Z","timestamp":1790000165000},"page":"e274209","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":0,"title":["Asynchronous bilateral pulmonary pathology: left-sided congenital pulmonary airway malformation with contralateral malignant pleuropulmonary blastoma in an adolescent"],"prefix":"10.1136","volume":"19","author":[{"given":"Ranganath T","family":"Ganga","sequence":"first","affiliation":[{"name":"Pulmonary, Critical Care and Sleep Medicine, All India Institute of Medical Sciences, Raipur, Chhatisgarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Praveen Kumar","family":"Dubey","sequence":"additional","affiliation":[{"name":"Pulmonary, Critical Care and Sleep Medicine, All India Institute of Medical Sciences, Raipur, Chhatisgarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mudalsha","family":"Ravina","sequence":"additional","affiliation":[{"name":"Nuclear Medicine, All India Institute of Medical Sciences, Raipur, Chhatisgarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2973-1793","authenticated-orcid":false,"given":"Ajay Kumar","family":"Verma","sequence":"additional","affiliation":[{"name":"King George\u2019s Medical University, Lucknow, Uttar Pradesh, India"},{"name":"Respiratory Medicine, Dr Ram Manohar Lohia Institute of Medical Sciences, Lucknow, Uttar Pradesh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bhoomika","family":"Kaushik","sequence":"additional","affiliation":[{"name":"Pathology and Lab Medicine, AIl India Institute of Medical Sciences, Raipur, Chhatisgarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ajoy","family":"Behera","sequence":"additional","affiliation":[{"name":"Pulmonary, Critical Care and Sleep Medicine, All India Institute of Medical Sciences, Raipur, Chhatisgarh, India"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[2026,9,21]]},"reference":[{"key":"2026092107151864000_19.9.e274209.1","doi-asserted-by":"crossref","first-page":"1559","DOI":"10.1007\/s00431-017-3032-7","article-title":"Congenital pulmonary airway malformations: state-of-the-art review for pediatrician\u2019s use","volume":"176","author":"Leblanc","year":"2017","journal-title":"Eur J Pediatr"},{"key":"2026092107151864000_19.9.e274209.2","doi-asserted-by":"publisher","DOI":"10.1148\/rg.2018180192"},{"key":"2026092107151864000_19.9.e274209.3","doi-asserted-by":"publisher","DOI":"10.1002\/cncr.29032"},{"key":"2026092107151864000_19.9.e274209.4","article-title":"Current Management of Pleuropulmonary Blastoma: A Surgical Perspective","volume":"6","author":"Knight","year":"2019","journal-title":"Children (Basel)"},{"key":"2026092107151864000_19.9.e274209.5","doi-asserted-by":"crossref","first-page":"70","DOI":"10.4103\/0971-5851.203515","article-title":"A Case Report of Pleuropulmonary Blastoma Presenting as Tension Pneumothorax","volume":"38","author":"Addanki","year":"2017","journal-title":"Indian J Med Paediatr Oncol"},{"key":"2026092107151864000_19.9.e274209.6","doi-asserted-by":"publisher","DOI":"10.1038\/s41379-021-00905-8"},{"key":"2026092107151864000_19.9.e274209.7","doi-asserted-by":"publisher","DOI":"10.1158\/1078-0432.Ccr-24-1532"},{"key":"2026092107151864000_19.9.e274209.8","doi-asserted-by":"crossref","first-page":"48","DOI":"10.1097\/MOP.0000000000001431","article-title":"Pleuropulmonary blastoma and DICER1-related tumor predisposition: from clinicopathologic observations to clinical trial","volume":"37","author":"Nelson","year":"2025","journal-title":"Curr Opin Pediatr"},{"key":"2026092107151864000_19.9.e274209.9","first-page":"231","article-title":"Pleuro-pulmonary blastoma presenting as a chest wall deformity: a case report","volume":"89","author":"S\u00e1ez B","year":"2018","journal-title":"Rev Chil Pediatr"},{"key":"2026092107151864000_19.9.e274209.10","doi-asserted-by":"crossref","first-page":"375","DOI":"10.1007\/s00428-020-02789-6","article-title":"Pleuropulmonary blastoma type I might arise in congenital pulmonary airway malformation type 4 by acquiring a Dicer 1 mutation","volume":"477","author":"Brcic","year":"2020","journal-title":"Virchows Arch"},{"key":"2026092107151864000_19.9.e274209.11","doi-asserted-by":"crossref","DOI":"10.1002\/pbc.29045","article-title":"Pleuropulmonary blastoma in children and adolescents: The EXPeRT\/PARTNER diagnostic and therapeutic recommendations","volume":"68 Suppl 4","author":"Bisogno","year":"2021","journal-title":"Pediatr Blood Cancer"}],"container-title":["BMJ Case Reports"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/bcr-2026-274209","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,9,21]],"date-time":"2026-09-21T14:16:07Z","timestamp":1790000167000},"score":1,"resource":{"primary":{"URL":"https:\/\/casereports.bmj.com\/lookup\/doi\/10.1136\/bcr-2026-274209"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,9]]},"references-count":11,"journal-issue":{"issue":"9","published-online":{"date-parts":[[2026,9,21]]},"published-print":{"date-parts":[[2026,9]]}},"alternative-id":["10.1136\/bcr-2026-274209"],"URL":"https:\/\/doi.org\/10.1136\/bcr-2026-274209","relation":{},"ISSN":["1757-790X"],"issn-type":[{"value":"1757-790X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,9]]}}}