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There is evidence that some children (and perhaps all) originally diagnosed with a deficiency of long-chain acyl-CoA dehydrogenase, in fact, have a defect involving very long chain acyl-CoA dehydrogenase.<\/jats:p>","DOI":"10.1136\/fn.73.2.f103","type":"journal-article","created":{"date-parts":[[2008,10,31]],"date-time":"2008-10-31T17:55:51Z","timestamp":1225475751000},"page":"F103-F105","source":"Crossref","is-referenced-by-count":23,"title":["Mitochondrial very long chain acyl-CoA dehydrogenase deficiency--a new disorder of fatty acid oxidation."],"prefix":"10.1136","volume":"73","author":[{"given":"C.","family":"Largilli\u00e8re","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C.","family":"Vianey-Saban","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M.","family":"Fontaine","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C.","family":"Bertrand","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"N.","family":"Kacet","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J. 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A novel disease with deficiency of mitochondrial very-long-chain acyl-CoA dehydrogenase. Biochem Biophys Res Commun 1993; 191: 1369-72.","journal-title":"Biochem Biophys Res Commun"},{"key":"ref_6","doi-asserted-by":"crossref","first-page":"111","DOI":"10.1203\/00006450-199307000-00025","article-title":"Identification of very-long-chain acyl-CoA dehydrogenase deficiency in three patients previously diagnosed with longchain acyl-CoA dehydrogenase deficiency","volume":"34","author":"Yamaguchi, S.; Indo, Y.; Coates, P.M.; Hashimoto, T.; Tanaka, K.","year":"1993","unstructured":"Yamaguchi S, Indo Y, Coates PM, Hashimoto T, Tanaka K. Identification of very-long-chain acyl-CoA dehydrogenase deficiency in three patients previously diagnosed with longchain acyl-CoA dehydrogenase deficiency. Pediatr Res 1993; 34: 111-3.","journal-title":"Pediatr Res"}],"container-title":["Archives of Disease in Childhood - Fetal and Neonatal Edition"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/fn.73.2.F103","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,9,5]],"date-time":"2025-09-05T21:17:02Z","timestamp":1757107022000},"score":1,"resource":{"primary":{"URL":"https:\/\/fn.bmj.com\/lookup\/doi\/10.1136\/fn.73.2.F103"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1995,9]]},"references-count":6,"journal-issue":{"issue":"2","published-online":{"date-parts":[[1995,9,1]]},"published-print":{"date-parts":[[1995,9]]}},"alternative-id":["10.1136\/fn.73.2.F103"],"URL":"https:\/\/doi.org\/10.1136\/fn.73.2.f103","relation":{},"ISSN":["1359-2998","1468-2052"],"issn-type":[{"type":"print","value":"1359-2998"},{"type":"electronic","value":"1468-2052"}],"subject":[],"published":{"date-parts":[[1995,9]]}}}