{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,18]],"date-time":"2025-10-18T07:10:50Z","timestamp":1760771450976,"version":"build-2065373602"},"reference-count":9,"publisher":"BMJ","issue":"1","content-domain":{"domain":["bmj.com"],"crossmark-restriction":true},"short-container-title":["Heart"],"accepted":{"date-parts":[[1997,7,25]]},"published-print":{"date-parts":[[1998,1,1]]},"abstract":"<jats:p>A male infant with the rare lesion of unguarded tricuspid orifice in the setting of pulmonary valve atresia, intact ventricular septum, and a hypoplastic right ventricle is described. The patient presented with cyanosis at 1 day old; transcutaneous oxygen saturations were between 20% and 30% in room air, and 60% in 100% inspired oxygen. Pre-excitation was found incidentally on the ECG and the potential for rapid antegrade conduction of atrial tachyarrhythmias, after eventual extended palliation with the Fontan procedure, was demonstrated at electrophysiological study. By 11 months old the patient was becoming increasingly cyanosed and interim palliation with a bidirectional cavopulmonary shunt was proposed. Successful radiofrequency ablation of the accessory pathway was performed before bidirectional cavopulmonary shunt, which would have prevented access to the heart via the superior vena cava. Difficulty with femoral venous access because of previous occlusion of a femoral vein was overcome by the use of 2\u2009F pacing electrodes and a 5\u2009F ablation catheter.<\/jats:p>","DOI":"10.1136\/hrt.79.1.101","type":"journal-article","created":{"date-parts":[[2014,10,22]],"date-time":"2014-10-22T15:31:45Z","timestamp":1413991905000},"page":"101-103","update-policy":"https:\/\/doi.org\/10.1136\/crossmarkpolicy","source":"Crossref","is-referenced-by-count":7,"title":["Unguarded tricuspid orifice with pulmonary atresia: successful radiofrequency ablation of an accessory pathway in an infant"],"prefix":"10.1136","volume":"79","author":[{"given":"Alan G","family":"Magee","sequence":"first","affiliation":[{"name":"aDepartment of Paediatric Cardiology, 11th Floor, Guy\u2019s Tower, Guy\u2019s Hospital, St Thomas Street, London SE1 9RT, UK, \n\nbDepartment of Adult Cardiology"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Eric","family":"Rosenthal","sequence":"additional","affiliation":[{"name":"aDepartment of Paediatric Cardiology, 11th Floor, Guy\u2019s Tower, Guy\u2019s Hospital, St Thomas Street, London SE1 9RT, UK, \n\nbDepartment of Adult Cardiology"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Julian","family":"Bostock","sequence":"additional","affiliation":[{"name":"aDepartment of Paediatric Cardiology, 11th Floor, Guy\u2019s Tower, Guy\u2019s Hospital, St Thomas Street, London SE1 9RT, UK, \n\nbDepartment of Adult Cardiology"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jaswinder","family":"Gill","sequence":"additional","affiliation":[{"name":"aDepartment of Paediatric Cardiology, 11th Floor, Guy\u2019s Tower, Guy\u2019s Hospital, St Thomas Street, London SE1 9RT, UK, \n\nbDepartment of Adult Cardiology"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[1998,1,1]]},"reference":[{"key":"2025101723280131000_79.1.101.1","doi-asserted-by":"publisher","DOI":"10.1136\/hrt.36.5.417"},{"key":"2025101723280131000_79.1.101.2","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9149(82)90048-0"},{"key":"2025101723280131000_79.1.101.3","doi-asserted-by":"crossref","first-page":"847","DOI":"10.1016\/S0022-5223(19)39599-6","article-title":"Surgical treatment of tachyarrhythmias in patients with both an Ebstein anomaly and a Kent bundle.","volume":"75","author":"Sealy","year":"1978","journal-title":"J Thorac Cardiovasc Surg"},{"key":"2025101723280131000_79.1.101.4","doi-asserted-by":"publisher","DOI":"10.1016\/0002-9149(93)90886-H"},{"key":"2025101723280131000_79.1.101.5","doi-asserted-by":"crossref","first-page":"911","DOI":"10.1161\/01.CIR.30.6.911","article-title":"Congenitally unguarded tricuspid orifice with co-existent pulmonary atresia.","volume":"30","author":"Kanjuh","year":"1964","journal-title":"Circulation"},{"key":"2025101723280131000_79.1.101.6","doi-asserted-by":"publisher","DOI":"10.1007\/BF02239568"},{"key":"2025101723280131000_79.1.101.7","doi-asserted-by":"crossref","first-page":"1","DOI":"10.1007\/BF02595067","article-title":"\u00dcber einen seltenen Fall von herzmissbildung mit rudiment\u00e4rer entwicklung des rechten ventrikels und defekt der tricuspidalklappen.","volume":"310","author":"Klein","year":"1938","journal-title":"Virchows Arch"},{"key":"2025101723280131000_79.1.101.8","doi-asserted-by":"crossref","first-page":"125","DOI":"10.1016\/0167-5273(96)02747-7","article-title":"Unguarded tricuspid orifice: a rare malformation of tricuspid valve diagnosed by echocardiography. Report of two cases and review of the literature.","volume":"56","author":"\u00d6zkutlu","year":"1996","journal-title":"Int J Cardiol"},{"key":"2025101723280131000_79.1.101.9","doi-asserted-by":"publisher","DOI":"10.1016\/0735-1097(94)90181-3"}],"container-title":["Heart"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/hrt.79.1.101","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,10,18]],"date-time":"2025-10-18T06:28:10Z","timestamp":1760768890000},"score":1,"resource":{"primary":{"URL":"https:\/\/heart.bmj.com\/lookup\/doi\/10.1136\/hrt.79.1.101"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1998,1,1]]},"references-count":9,"journal-issue":{"issue":"1","published-online":{"date-parts":[[1998,1,1]]},"published-print":{"date-parts":[[1998,1,1]]}},"alternative-id":["10.1136\/hrt.79.1.101"],"URL":"https:\/\/doi.org\/10.1136\/hrt.79.1.101","relation":{},"ISSN":["1355-6037","1468-201X"],"issn-type":[{"type":"print","value":"1355-6037"},{"type":"electronic","value":"1468-201X"}],"subject":[],"published":{"date-parts":[[1998,1,1]]}}}