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In the absence of cutaneous signs, however, the diagnosis is less obvious. The case reported had predominantly marrow and splenic involvement by the disease process, giving rise to portal hypertension, and illustrates the problems of diagnosis which can arise.<\/jats:p>","DOI":"10.1136\/jcp.35.6.617","type":"journal-article","created":{"date-parts":[[2007,6,9]],"date-time":"2007-06-09T00:50:46Z","timestamp":1181350246000},"page":"617-619","source":"Crossref","is-referenced-by-count":18,"title":["Systemic mastocytosis, myelofibrosis and portal hypertension."],"prefix":"10.1136","volume":"35","author":[{"given":"A H","family":"Sawers","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J","family":"Davson","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J","family":"Braganza","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C G","family":"Geary","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","published-online":{"date-parts":[[1982,6,1]]},"reference":[{"key":"ref_1","first-page":"323","article-title":"Rare forms of urticaria","volume":"ii:","author":"Nettleship, E.","unstructured":"Nettleship E. 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