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Complications of HHT are discussed and an age of onset curve given.<\/jats:p>","DOI":"10.1136\/jmg.29.8.527","type":"journal-article","created":{"date-parts":[[2008,11,10]],"date-time":"2008-11-10T15:23:16Z","timestamp":1226330596000},"page":"527-530","source":"Crossref","is-referenced-by-count":165,"title":["Hereditary haemorrhagic telangiectasia: a clinical analysis."],"prefix":"10.1136","volume":"29","author":[{"given":"M E","family":"Porteous","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J","family":"Burn","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"S J","family":"Proctor","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"239","published-online":{"date-parts":[[1992,8,1]]},"reference":[{"key":"ref_1","first-page":"63","article-title":"Multiple hereditary telangiectasis causing hemorrhage (hereditary hemorrhagic telangiectasia). Bull J7ohns Hopkins Hosp 1909; 20","author":"Hanes, F.M.","unstructured":"Hanes FM. Multiple hereditary telangiectasis causing hemorrhage (hereditary hemorrhagic telangiectasia). Bull J7ohns Hopkins Hosp 1909;20:63-73."},{"key":"ref_2","first-page":"769","article-title":"Epistaxis as an indication of impaired nutrition and of degeneration of the vascular system","volume":"1","author":"Sutton, H.G.","year":"1864","unstructured":"Sutton HG. Epistaxis as an indication of impaired nutrition and of degeneration of the vascular system. Med Mirror 1864;1:769.","journal-title":"Med Mirror"},{"issue":"12","key":"ref_3","first-page":"333","article-title":"On a family form of recurring epistaxis associated with multiple telangiectases of the skin and mucous membranes","volume":"1901","author":"Osler, W.","unstructured":"Osler W. On a family form of recurring epistaxis associated with multiple telangiectases of the skin and mucous membranes. 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Clinical and experimental studies in human inheritance: is the homozygous form of multiple telangiectasia lethal? Lab Clin Med 1944;29:1211-6.","journal-title":"Lab Clin Med"},{"key":"ref_10","doi-asserted-by":"crossref","first-page":"522","DOI":"10.1001\/archotol.1965.00760010524014","article-title":"Hereditary hemorrhagic telangiectasia; review of 102 cases and presentation of an innovation to septodermoplasty","volume":"82","author":"Stecker, R.H.; Lake, C.F.","year":"1965","unstructured":"Stecker RH, Lake CF. Hereditary hemorrhagic telangiectasia; review of 102 cases and presentation of an innovation to septodermoplasty. Arch Otolaryngol 1965;82:522-6.","journal-title":"Arch Otolaryngol"},{"key":"ref_11","doi-asserted-by":"crossref","first-page":"105","DOI":"10.1111\/j.0954-6820.1985.tb08832.x","article-title":"Pulmonary arteriovenous fistulas in hereditary hemorrhagic telangiectasia","volume":"218","author":"Vase, P.; Holm, M.; Arendrup, H.","year":"1985","unstructured":"Vase P, Holm M, Arendrup H. Pulmonary arteriovenous fistulas in hereditary hemorrhagic telangiectasia. Acta Med Scand 1985;218:105-9.","journal-title":"Acta Med Scand"},{"key":"ref_12","doi-asserted-by":"crossref","first-page":"151","DOI":"10.1007\/BF02552883","article-title":"Cerebral embolism - first manifestation of pulmonary arteriovenous malformation in patients with hereditary hemorrhagic telangiectasia","volume":"8","author":"Hewes, R.C.; Auster, M.; White, R.I.","year":"1985","unstructured":"Hewes RC, Auster M, White RI. 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Pulmonary arteriovenous malformations: techniques and long-term outcome of embolotherapy. Radiology 1988;169:663-9.","journal-title":"Radiology"},{"key":"ref_15","first-page":"791","article-title":"Fiberoptic bronchoscope and Nd-YAG laser treatment of severe epistaxis from nasal hereditary hemorrhagic telangiectasia and hemangioma","volume":"91","author":"Mehta, A.C.; Livingston, D.R.; Levine, H.L.","year":"1990","unstructured":"Mehta AC, Livingston DR, Levine HL. Fiberoptic bronchoscope and Nd-YAG laser treatment of severe epistaxis from nasal hereditary hemorrhagic telangiectasia and hemangioma. 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