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Although mental deficiency is known in association with familial ataxia or spastic paraplegia beginning in childhood, the family reported by Akelaitis'9 was an example showing severe dementia with ataxia. However the pathology in this family is uncertain."},{"key":"ref_4","first-page":"796","article-title":"pathology","year":"1976","unstructured":"pathology, 3rd ed. London: Edward Arnold, 1976: 796-848.","edition":"3rd ed"},{"key":"ref_5","article-title":"Jakob-Creutzfeldt Disease","author":"Kirschbaum, W.R.","year":"1968","unstructured":"Kirschbaum WR. Jakob-Creutzfeldt Disease. 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