{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,20]],"date-time":"2025-10-20T17:53:39Z","timestamp":1760982819358},"reference-count":17,"publisher":"BMJ","issue":"3","content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Journal of Neurology, Neurosurgery &amp; Psychiatry"],"published-print":{"date-parts":[[1985,3,1]]},"DOI":"10.1136\/jnnp.48.3.234","type":"journal-article","created":{"date-parts":[[2008,11,10]],"date-time":"2008-11-10T21:16:40Z","timestamp":1226351800000},"page":"234-238","source":"Crossref","is-referenced-by-count":19,"title":["Familial clustering of the ataxic form of Creutzfeldt-Jakob disease with Hirano bodies."],"prefix":"10.1136","volume":"48","author":[{"given":"L","family":"Cartier","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S","family":"Galvez","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"D C","family":"Gajdusek","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"239","reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"350","DOI":"10.1136\/jnnp.28.4.350","article-title":"An ataxic form of subacute presenile polioencephalopathy (CreutzfeldtJakob disease)","volume":"28","year":"1965","unstructured":"Brownell B, Oppenheimer DR. An ataxic form of subacute presenile polioencephalopathy (CreutzfeldtJakob disease). J Neurol Neurosurg Psychiatry 1965;28:350-61.","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"ref_2","first-page":"559","article-title":"CreutzfeldtJakob disease virus isolations from the GerstmannStraussler syndrome, with an analysis of the various forms of amyloid plaque deposition in the virusinduced spongiform encephalopathies","volume":"104","author":"Masters, C.L.; Gajdusek, D.C.; CJ, Jr, Gibbs","year":"1981","unstructured":"Masters CL, Gajdusek DC, Gibbs CJ Jr. CreutzfeldtJakob disease virus isolations from the GerstmannStraussler syndrome, with an analysis of the various forms of amyloid plaque deposition in the virusinduced spongiform encephalopathies. Brain 1981; 104:559-88.","journal-title":"Brain"},{"key":"ref_3","first-page":"137","article-title":"Creutzfeldt-Jakob disease with kuru-like neuropathological features","volume":"3","author":"Cartier, L.; Martin, S.; Galvez, S.","year":"1982","unstructured":"Cartier L, Martin S, Galvez S. Creutzfeldt-Jakob disease with kuru-like neuropathological features. Phronesis 1982;3: 137-46.","journal-title":"Phronesis"},{"key":"ref_4","doi-asserted-by":"crossref","first-page":"291","DOI":"10.1016\/0022-510X(79)90122-9","article-title":"Kuru plaques in the brain of two cases with Creutzfeldt-Jakob disease","volume":"43","author":"Zarranz, J.J.; Rivera-Pomar, J.M.; Salisachs, P.","year":"1979","unstructured":"Zarranz JJ, Rivera-Pomar JM, Salisachs P. Kuru plaques in the brain of two cases with Creutzfeldt-Jakob disease. J Neurol Sci 1979;43:291-300.","journal-title":"J Neurol Sci"},{"key":"ref_5","doi-asserted-by":"crossref","first-page":"419","DOI":"10.1016\/0013-4694(73)90093-X","article-title":"The EEG of kuru","volume":"34","author":"Cobb, W.; Hornabrook, R.W.; Sanders, S.","year":"1973","unstructured":"Cobb W, Hornabrook RW, Sanders S. The EEG of kuru. Electroencephologr Clin Neurophysiol 1973;34:419-27.","journal-title":"Electroencephologr Clin Neurophysiol"},{"key":"ref_6","first-page":"359","article-title":"Virus-induced subacute slow infections of the brain associated with a cerebellartype ataxia","volume-title":"Advances in Neurology. Vol 21","author":"CJ, Jr, Gibbs; DC, Gajdusek","year":"1978","unstructured":"Gibbs CJ Jr, Gajdusek DC. Virus-induced subacute slow infections of the brain associated with a cerebellartype ataxia. In: Kark RAP, Rosemberg RN, Schut LJ, eds. Advances in Neurology. Vol 21. New York: Raven Press, 1978:359-72."},{"key":"ref_7","first-page":"575","article-title":"Encephalopathie spongieuse tardive de type Creutzfeldt-Jakob avec importantes lesions cerebelleuses (Etude anatomo-clinique d'un cas)","volume":"49","author":"Michel, D.; Tommasi, M.; Masson, R.; Rochet, M.; Berthezene, F.; Schott, B.","year":"1968","unstructured":"Michel D, Tommasi M, Masson R, Rochet M, Berthezene F, Schott B. Encephalopathie spongieuse tardive de type Creutzfeldt-Jakob avec importantes lesions cerebelleuses (Etude anatomo-clinique d'un cas). J Med Lyon 1968;49:575-92.","journal-title":"J Med Lyon"},{"key":"ref_8","first-page":"73","article-title":"Maladie de Creutzfeldt-Jakob a symptomatologie cerebelleuse dominante (Etude anatomo-clinique d'un cas)","volume":"113","author":"Boudin, G.; Pepin, B.; Milhaud, M.","year":"1965","unstructured":"Boudin G, Pepin B, Milhaud M. Maladie de Creutzfeldt-Jakob a symptomatologie cerebelleuse dominante (Etude anatomo-clinique d'un cas). Rev Neurol (Paris) 1965;113:73-5.","journal-title":"Rev Neurol (Paris)"},{"key":"ref_9","doi-asserted-by":"crossref","first-page":"107","DOI":"10.1016\/0022-510X(67)90011-1","article-title":"Ataxic form of Creutzfeldt-Jakob disease. Its relation to subacute spongiform encephalopathy","volume":"5","author":"Kott, E.; Bornstein, B.; Sandbank, U.","year":"1967","unstructured":"Kott E, Bornstein B, Sandbank U. Ataxic form of Creutzfeldt-Jakob disease. Its relation to subacute spongiform encephalopathy. J Neurol Sci 1967; 5:107-13.","journal-title":"J Neurol Sci"},{"key":"ref_10","doi-asserted-by":"crossref","first-page":"61","DOI":"10.1007\/BF00688000","article-title":"A study of rodlike structures (Hirano bodies) in 240 normal and pathological brains","volume":"21","author":"Ogata, J.; Budzilovich, G.N.; Cravioto, H.","year":"1972","unstructured":"Ogata J, Budzilovich GN, Cravioto H. A study of rodlike structures (Hirano bodies) in 240 normal and pathological brains. Acta Neuropathol (Berl) 1972;21:61-7.","journal-title":"Acta Neuropathol (Berl)"},{"key":"ref_11","doi-asserted-by":"crossref","first-page":"35","DOI":"10.1001\/archneur.1966.00470130039004","article-title":"Amyotrophic lateral sclerosis and Parkinsonism-dementia complex on","volume":"15","year":"1966","unstructured":"Hirano A, Malamud N, Elizan TS, Kurland LT. Amyotrophic lateral sclerosis and Parkinsonism-dementia complex on Guam. Arch Neurol 1966; 15:35-51.","journal-title":"Guam. Arch Neurol"},{"key":"ref_12","first-page":"1093","article-title":"Altered synaptic terminals in cortex near tumor","volume":"51","author":"Ramsey, M.J.","year":"1967","unstructured":"Ramsey MJ. Altered synaptic terminals in cortex near tumor. Am J Pathol 1967;51:1093-1109.","journal-title":"Am J Pathol"},{"key":"ref_13","doi-asserted-by":"crossref","first-page":"548","DOI":"10.1001\/archneur.1969.00480110112012","article-title":"Intraneuronal conglomerates in sporadic motor neuron disease","volume":"20","year":"1969","unstructured":"Intraneuronal conglomerates in sporadic motor neuron disease. Arch Neurol 1969;20:548-53.","journal-title":"Arch Neurol"},{"key":"ref_14","first-page":"159","article-title":"Abundant eosinophilic rod-like structures in subacute spongiform encephalopathy","volume":"46","author":"Llena, J.F.; Hirano, A.","year":"1979","unstructured":"Llena JF, Hirano A. Abundant eosinophilic rod-like structures in subacute spongiform encephalopathy. J Neuropathol Exp Neurol 1979;38:329. '5 Flament-Durand J, Couck AM. Spongiform alterations in brain biopsies of presenile dementia. Acta Neuropathol (Berl) 1979;46:159-62.","journal-title":"J Neuropathol Exp Neurol; 38: 329. '5 Flament-Durand J, Couck AM. Spongiform alterations in brain biopsies of presenile dementia"},{"key":"ref_15","first-page":"313","article-title":"Scrapie in mice. Ultrastructural observations","volume-title":"the cerebral cortex. Proc Soc Exp Biol Med 1968","volume":"127","author":"David-Ferreira, J.F.; David-Ferreira, K.L.; CJ, Jr, Gibbs; Morris, J.A.","unstructured":"David-Ferreira JF, David-Ferreira KL, Gibbs CJ Jr, Morris JA. Scrapie in mice. Ultrastructural observations in the cerebral cortex. Proc Soc Exp Biol Med 1968; 127:313-20."},{"key":"ref_16","doi-asserted-by":"crossref","first-page":"209","DOI":"10.1016\/0022-510X(69)90111-7","article-title":"Electron microscopic observations on the cerebellar cortex in Kuru","volume":"8","author":"Field, E.J.; Mathews, J.D.; Raine, C.S.","year":"1969","unstructured":"Field EJ, Mathews JD, Raine CS. Electron microscopic observations on the cerebellar cortex in Kuru. J Neurol Sci 1969;8:209-24.","journal-title":"J Neurol Sci"},{"key":"ref_17","doi-asserted-by":"crossref","first-page":"139","DOI":"10.1016\/0022-510X(83)90087-4","article-title":"Familial Creutzfeldt-Jakob disease in Chile","volume":"59","author":"Galvez, S.; Cartier, L.; Monari, M.; Araya, G.","year":"1983","unstructured":"Galvez S, Cartier L, Monari M, Araya G. Familial Creutzfeldt-Jakob disease in Chile. J Neurol Sci 1983;59: 139-47.","journal-title":"J Neurol Sci"}],"container-title":["Journal of Neurology, Neurosurgery &amp; Psychiatry"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/jnnp.48.3.234","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,9,26]],"date-time":"2020-09-26T04:08:43Z","timestamp":1601093323000},"score":1,"resource":{"primary":{"URL":"https:\/\/jnnp.bmj.com\/lookup\/doi\/10.1136\/jnnp.48.3.234"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1985,3,1]]},"references-count":17,"journal-issue":{"issue":"3","published-print":{"date-parts":[[1985,3,1]]}},"URL":"https:\/\/doi.org\/10.1136\/jnnp.48.3.234","relation":{},"ISSN":["0022-3050"],"issn-type":[{"value":"0022-3050","type":"print"}],"subject":[],"published":{"date-parts":[[1985,3,1]]}}}