{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,21]],"date-time":"2026-03-21T19:32:06Z","timestamp":1774121526970,"version":"3.50.1"},"reference-count":7,"publisher":"Oxford University Press (OUP)","issue":"660","license":[{"start":{"date-parts":[[1980,10,1]],"date-time":"1980-10-01T00:00:00Z","timestamp":339206400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/academic.oup.com\/pages\/standard-publication-reuse-rights"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[1980,10,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n               <jats:p>Marfan\u2019s syndrome is a rare hereditary disorder characterized by skeletal, cardiovascular and ocular abnormalities. Pulmonary abnormalities occur in approximately 10% of patients the commonest being spontaneous pneumothorax and emphysema. A patient is described who had Marfan\u2019s syndrome and bronchiectasis, an association only described on 2 previous occasions in the literature.<\/jats:p>","DOI":"10.1136\/pgmj.56.660.718","type":"journal-article","created":{"date-parts":[[2008,12,29]],"date-time":"2008-12-29T20:39:26Z","timestamp":1230583166000},"page":"718-719","source":"Crossref","is-referenced-by-count":25,"title":["Bronchiectasis and Marfan\u2019s syndrome"],"prefix":"10.1093","volume":"56","author":[{"given":"M E","family":"Foster","sequence":"first","affiliation":[{"name":"Department of Cardio-thoracic Surgery, University Hospital of Wales , Cardiff"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"D R","family":"Foster","sequence":"additional","affiliation":[{"name":"Department of Radiology, University Hospital of Wales , Cardiff"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[1980,10,1]]},"reference":[{"key":"ref_1","doi-asserted-by":"crossref","first-page":"1285","DOI":"10.7326\/0003-4819-62-6-1285","article-title":"Spontanieous pneumothorax and pulmonary disease in Marfan's syndrome","volume":"62","author":"DWYER Jr, E. M. & TROWCALE, F","year":"1965","unstructured":"DWYER Jr, E.M. & TROWCALE, F. (1965) Spontanieous pneumothorax and pulmonary disease in Marfan's syndrome. Annals of Internal Medicine. 62, 1285.","journal-title":"Annals of Internal Medicine"},{"key":"ref_2","first-page":"299","article-title":"Arachnodactylia","volume":"50","author":"GREEN, H.; EMERSON, P.W.","year":"1943","unstructured":"GREEN, H. & EMERSON, P.W. (1943) Arachnodactylia. Archives of Pediatrics, 50, 299.","journal-title":"Archives of Pediatrics"},{"key":"ref_3","first-page":"95","article-title":"Thoracic manifestation in Marfan's syndrome (arachnodactyly)","volume":"13","author":"KATZ, H.L.","year":"1952","unstructured":"KATZ, H.L. (1952) Thoracic manifestation in Marfan's syndrome (arachnodactyly). Quarterly Bulletin of Sea View Hospital, 13, 95.","journal-title":"Quarterly Bulletin of Sea View Hospital"},{"key":"ref_4","first-page":"1","article-title":"Honeycomb lungs","volume":"18","author":"OSWALD, N.; PARKINSON, T.","year":"1949","unstructured":"OSWALD, N. & PARKINSON, T. (1949) Honeycomb lungs. Quarterly Journal of Medicine, 18, 1.","journal-title":"Quarterly Journal of Medicine"},{"key":"ref_5","doi-asserted-by":"crossref","first-page":"672","DOI":"10.1378\/chest.72.5.672","article-title":"Bronchiectasis and spontaneous pneumothorax in Marfan's syndrome","volume":"72","author":"TEOH, P.C.","year":"1977","unstructured":"TEOH, P.C. (1977) Bronchiectasis and spontaneous pneumothorax in Marfan's syndrome. Chest, 72, 672.","journal-title":"Chest"},{"key":"ref_6","doi-asserted-by":"crossref","first-page":"771","DOI":"10.1136\/thx.31.6.771","article-title":"Fragile lung in the Marfan syndrome","volume":"31","author":"TURNER, J.A.M.C.M.; STANLEY, N.N.","year":"1976","unstructured":"TURNER, J.A. MCM. & STANLEY, N.N. (1976) Fragile lung in the Marfan syndrome. Thiorax, 31, 771.","journal-title":"Thiorax"},{"key":"ref_7","article-title":"Cardiovascular disease in arachnodactyly","volume":"161","author":"BUCHEM, V.A.N.; P, F.S.","year":"1958","unstructured":"VAN BUCHEM, F.S.P. (1958) Cardiovascular disease in arachnodactyly. 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